The process of mammalian mitochondrial protein synthesis von Mai, Nicole, Chrzanowska-Lightowlers, Zofia M. A., Lightowlers, Robert N.

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Human mitochondrial nucleases von Bruni, Francesco, Lightowlers, Robert N., Chrzanowska‐Lightowlers, Zofia M.

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Messenger RNA delivery to mitoribosomes – hints from a bacterial toxin von Bruni, Francesco, Proctor‐Kent, Yasmin, Lightowlers, Robert N., Chrzanowska‐Lightowlers, Zofia M.

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Human ERAL1 is a mitochondrial RNA chaperone involved in the assembly of the 28S small mitochondrial ribosomal subunit von Dennerlein, Sven, Rozanska, Agata, Wydro, Mateusz, Chrzanowska-Lightowlers, Zofia M A, Lightowlers, Robert N

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Pathogenic variants in HTRA2 cause an early-onset mitochondrial syndrome associated with 3-methylglutaconic aciduria von Oláhová, Monika, Thompson, Kyle, Hardy, Steven A., Barbosa, Inês A., Besse, Arnaud, Anagnostou, Maria-Eleni, White, Kathryn, Davey, Tracey, Simpson, Michael A., Champion, Michael, Enns, Greg, Schelley, Susan, Lightowlers, Robert N., Chrzanowska-Lightowlers, Zofia M. A., McFarland, Robert, Deshpande, Charu, Bonnen, Penelope E., Taylor, Robert W.

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REXO2 is an oligoribonuclease active in human mitochondria von Bruni, Francesco, Gramegna, Pasqua, Oliveira, Jorge M A, Lightowlers, Robert N, Chrzanowska-Lightowlers, Zofia M A

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Mitochondrial transplantation—a possible therapeutic for mitochondrial dysfunction?: Mitochondrial transfer is a potential cure for many diseases but proof of efficacy and safety i... von Lightowlers, Robert N, Chrzanowska‐Lightowlers, Zofia MA, Russell, Oliver M

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Defective Mitochondrial mRNA Maturation Is Associated with Spastic Ataxia von Crosby, Andrew H., Patel, Heema, Chioza, Barry A., Proukakis, Christos, Gurtz, Kay, Patton, Michael A., Sharifi, Reza, Harlalka, Gaurav, Simpson, Michael A., Dick, Katherine, Reed, Johanna A., Al-Memar, Ali, Chrzanowska-Lightowlers, Zofia M.A., Cross, Harold E., Lightowlers, Robert N.

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GRSF1 Regulates RNA Processing in Mitochondrial RNA Granules von Jourdain, Alexis A., Koppen, Mirko, Wydro, Mateusz, Rodley, Chris D., Lightowlers, Robert N., Chrzanowska-Lightowlers, Zofia M., Martinou, Jean-Claude

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Nuclear factors involved in mitochondrial translation cause a subgroup of combined respiratory chain deficiency von KEMP, John P, SMITH, Paul M, CZERMIN, Birgit, LOCHMÜLLER, Hanns, MCFARLAND, Robert, CHINNERY, Patrick F, CHRZANOWSKA-LIGHTOWLERS, Zofia M. A, LIGHTOWLERS, Robert N, TAYLOR, Robert W, HORVATH, Rita, PYLE, Angela, NEEVE, Vivienne C. M, TUPPEN, Helen A. L, SCHARA, Ulrike, TALIM, Beril, TOPALOGLU, Haluk, HOLINSKI-FEDER, Elke, ABICHT, Angela

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Mitochondrial RNA maturation von Chrzanowska-Lightowlers, Zofia M, Lightowlers, Robert N

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The p.M292T NDUFS2 mutation causes complex I-deficient Leigh syndrome in multiple families von Tuppen, Helen A. L., Hogan, Vanessa E., He, Langping, Blakely, Emma L., Worgan, Lisa, Al-Dosary, Mazhor, Saretzki, Gabriele, Alston, Charlotte L., Morris, Andrew A., Clarke, Michael, Jones, Simon, Devlin, Anita M., Mansour, Sahar, Chrzanowska-Lightowlers, Zofia M. A., Thorburn, David R., McFarland, Robert, Taylor, Robert W.

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Salvaging hope: Is increasing NAD+ a key to treating mitochondrial myopathy? von Lightowlers, Robert N, Chrzanowska‐Lightowlers, Zofia MA

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High-resolution imaging reveals compartmentalization of mitochondrial protein synthesis in cultured human cells von Zorkau, Matthew, Albus, Christin A., Berlinguer-Palmini, Rolando, Chrzanowska-Lightowlers, Zofia M. A., Lightowlers, Robert N.

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Human mitochondrial leucyl tRNA synthetase can suppress non cognate pathogenic mt‐tRNA mutations von Hornig‐Do, Hue Tran, Montanari, Arianna, Rozanska, Agata, Tuppen, Helen A, Almalki, Abdulraheem A, Abg‐Kamaludin, Dyg P, Frontali, Laura, Francisci, Silvia, Lightowlers, Robert N, Chrzanowska‐Lightowlers, Zofia M

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Mitochondrial protein synthesis: Figuring the fundamentals, complexities and complications, of mammalian mitochondrial translation von Lightowlers, Robert N., Rozanska, Agata, Chrzanowska-Lightowlers, Zofia M.

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The Pseudouridine Synthase RPUSD4 Is an Essential Component of Mitochondrial RNA Granules von Zaganelli, Sofia, Rebelo-Guiomar, Pedro, Maundrell, Kinsey, Rozanska, Agata, Pierredon, Sandra, Powell, Christopher A., Jourdain, Alexis A., Hulo, Nicolas, Lightowlers, Robert N., Chrzanowska-Lightowlers, Zofia M., Minczuk, Michal, Martinou, Jean-Claude

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Defective mitochondrial protease LonP1 can cause classical mitochondrial disease von Peter, Bradley, Waddington, Christie L, Oláhová, Monika, Sommerville, Ewen W, Hopton, Sila, Pyle, Angela, Champion, Michael, Ohlson, Monica, Siibak, Triinu, Chrzanowska-Lightowlers, Zofia M A, Taylor, Robert W, Falkenberg, Maria, Lightowlers, Robert N

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SLIRP stabilizes LRPPRC via an RRM-PPR protein interface von Spåhr, Henrik, Rozanska, Agata, Li, Xinping, Atanassov, Ilian, Lightowlers, Robert N, Chrzanowska-Lightowlers, Zofia M A, Rackham, Oliver, Larsson, Nils-Göran

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Rescuing stalled mammalian mitoribosomes - what can we learn from bacteria? von Ayyub, Shreya Ahana, Gao, Fei, Lightowlers, Robert N., Chrzanowska-Lightowlers, Zofia M.

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