Outcome of pyruvate dehydrogenase deficiency treated with ketogenic diets : Studies in patients with identical mutations von WEXLER, I. D, HEMALATHA, S. G, MCCONNELL, J, BUIST, N. R. M, DAHL, H.-H. M, BERRY, S. A, CEDERBAUM, S. D, PATEL, M. S, KERR, D. S

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Biochemical characteristics of newborns with carnitine transporter defect identified by newborn screening in California von Gallant, N.M., Leydiker, K., Wilnai, Y., Lee, C., Lorey, F., Feuchtbaum, L., Tang, H., Carter, J., Enns, G.M., Packman, S., Lin, H.J., Wilcox, W.R., Cederbaum, S.D., Abdenur, J.E.

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Minimal ureagenesis is necessary for survival in the murine model of hyperargininemia treated by AAV-based gene therapy von Hu, C, Tai, D S, Park, H, Cantero, G, Chan, E, Yudkoff, M, Cederbaum, S D, Lipshutz, G S

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AAV-based gene therapy prevents neuropathology and results in normal cognitive development in the hyperargininemic mouse von Lee, E K, Hu, C, Bhargava, R, Ponnusamy, R, Park, H, Novicoff, S, Rozengurt, N, Marescau, B, De Deyn, P, Stout, D, Schlichting, L, Grody, W W, Cederbaum, S D, Lipshutz, G S

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Cloning and Characterization of the Human Type II Arginase Gene von Vockley, Joseph G., Jenkinson, Christopher P., Shukla, Hridayabiranjan, Kern, Rita M., Grody, Wayne W., Cederbaum, Stephen D.

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Hyperargininemia due to liver arginase deficiency von Crombez, Eric A., Cederbaum, Stephen D.

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Arginases I and II: do their functions overlap? von Cederbaum, Stephen D, Yu, Hong, Grody, Wayne W, Kern, Rita M, Yoo, Paul, Iyer, Ramaswamy K

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Minimal ureagenesis is necessary for survival in the murine model of hyperargininemia treated by AAV-based gene therapy von Hu, C, Tai, D S, Park, H, Cantero, G, Chan, E, Yudkoff, M, Cederbaum, S D, Lipshutz, G S

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Mouse Model for Human Arginase Deficiency von Iyer, Ramaswamy K., Yoo, Paul K., Kern, Rita M., Rozengurt, Nora, Tsoa, Rosemarie, O'Brien, William E., Yu, Hong, Grody, Wayne W., Cederbaum, Stephen D.

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Helicobacter pylori Induces Macrophage Apoptosis by Activation of Arginase II von Gobert, Alain P, Cheng, Yulan, Wang, Jian-Ying, Boucher, Jean-Luc, Iyer, Ramaswamy K, Cederbaum, Stephen D, Casero, Robert A., Jr, Newton, Jamie C, Wilson, Keith T

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SIDS and disorders of fatty acid oxidation: Where do we go from here? von Cederbaum, Stephen D.

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Comparative properties of arginases von Jenkinson, Christopher P., Grody, Wayne W., Cederbaum, Stephen D.

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Successful pregnancy outcome in a woman with argininosuccinate lyase deficiency von Mardach, M. R., Roe, K., Cederbaum, S. D.

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Spontaneous pneumothorax in association with pyridoxine‐responsive homocystinuria von Bass, H. N., LaGrave, D., Mardach, R., Cederbaum, S. D., Fuster, C. D., Chetty, M.

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Expression of arginase isozymes in mouse brain von Yu, Hong, Iyer, Ramaswamy K., Kern, Rita M., Rodriguez, Williams I., Grody, Wayne W., Cederbaum, Stephen D.

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Laboratory evaluation of urea cycle disorders von Steiner, Robert D., Cederbaum, Stephen D.

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Arginase induction by sodium phenylbutyrate in mouse tissues and human cell lines von Kern, R.M., Yang, Z., Kim, P.S., Grody, W.W., Iyer, R.K., Cederbaum, S.D.

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Psychosocial issues and coping strategies in families affected by urea cycle disorders von Cederbaum, Julie A., LeMons, Cynthia, Rosen, Mindy, Ahrens, Mary, Vonachen, Sharon, Cederbaum, Stephen D.

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Differential expression of the two human arginase genes in hyperargininemia: enzymatic, pathologic, and molecular analysis von GRODY, W. W, ARGYLE, C, KERN, R. M, DIZIKES, G. J, SPECTOR, E. B, STRICKLAND, A. D, KLEIN, D, CEDERBAUM, S. D

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Guanidino compound analysis as a complementary diagnostic parameter for hyperargininemia: follow-up of guanidino compound levels during therapy von MARESCAU, B, DE DEYN, P. P, HYLAND, K, GATTI, R, KANG, S. S, LETARTE, J, LAMBERT, M, MIZUTANI, N, POSSEMIERS, I, REZVANI, I, SNYDERMAN, S. E, TERHEGGEN, H. G, LOWENTHAL, A, QURESHI, I. A, ANTONOZZI, I, BACHMANN, C, CEDERBAUM, S. D, CERONE, R, CHAMOLES, N, COLOMBO, J. P

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