Membrane-bound CYB5R3 is a common effector of nutritional and oxidative stress response through FOXO3a and Nrf2 von Siendones, Emilio, SantaCruz-Calvo, Sara, Martín-Montalvo, Alejandro, Cascajo, María V, Ariza, Julia, López-Lluch, Guillermo, Villalba, José M, Acquaviva-Bourdain, Cécile, Roze, Emmanuel, Bernier, Michel, de Cabo, Rafael, Navas, Plácido

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Cellular Models for Primary CoQ Deficiency Pathogenesis Study von Santos-Ocana, Carlos, Cascajo, Maria V., Alcazar-Fabra, Maria, Staiano, Carmine, Lopez-Lluch, Guillermo, Brea-Calvo, Gloria, Navas, Placido

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Secondary coenzyme Q10 deficiencies in oxidative phosphorylation (OXPHOS) and non-OXPHOS disorders von Yubero, Delia, Montero, Raquel, Martín, Miguel A, Montoya, Julio, Ribes, Antonia, Grazina, Manuela, Trevisson, Eva, Rodriguez-Aguilera, Juan Carlos, Hargreaves, Iain P, Salviati, Leonardo, Navas, Plácido, Artuch, Rafael, Jou, Cristina, Jimenez-Mallebrera, Cecilia, Nascimento, Andres, Pérez-Dueñas, Belén, Ortez, Carlos, Ramos, Federico, Colomer, Jaume, O'Callaghan, Mar, Pineda, Mercè, García-Cazorla, Angels, Espinós, Carmina, Ruiz, Angels, Macaya, Alfons, Marcé-Grau, Anna, Garcia-Villoria, Judit, Arias, Angela, Emperador, Sonia, Ruiz-Pesini, Eduardo, Lopez-Gallardo, Ester, Neergheen, Viruna, Simões, Marta, Diogo, Luisa, Blázquez, Alberto, González-Quintana, Adrián, Delmiro, Aitor, Domínguez-González, Cristina, Arenas, Joaquín, García-Silva, M Teresa, Martín, Elena, Quijada, Pilar, Hernández-Laín, Aurelio, Morán, María, Rivas Infante, Eloy, Ávila Polo, Rainiero, Paradas Lópe, Carmen, Bautista Lorite, Juan, Martínez Fernández, Eva M, Cortés, Ana B, Sánchez-Cuesta, Ana, Cascajo, Maria V, Alcázar, María, Brea-Calvo, Gloria

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RNA-binding proteins regulate cell respiration and coenzyme Q biosynthesis by post-transcriptional regulation of COQ7 von Cascajo, María V., Abdelmohsen, Kotb, Noh, Ji Heon, Fernández-Ayala, Daniel J.M., Willers, Imke M., Brea, Gloria, López-Lluch, Guillermo, Valenzuela-Villatoro, Marina, Cuezva, José M., Gorospe, Myriam, Siendones, Emilio, Navas, Plácido

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Association between coenzyme Q10 and glucose transporter (GLUT1) deficiency von Yubero, Delia, O'Callaghan, Mar, Montero, Raquel, Ormazabal, Aida, Armstrong, Judith, Espinos, Carmina, Rodríguez, Maria A, Jou, Cristina, Castejon, Esperanza, Aracil, Maria A, Cascajo, Maria V, Gavilan, Angela, Briones, Paz, Jimenez-Mallebrera, Cecilia, Pineda, Mercedes, Navas, Plácido, Artuch, Rafael

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Survival transcriptome in the coenzyme Q10 deficiency syndrome is acquired by epigenetic modifications: a modelling study for human coenzyme Q10 deficiencies von Fernández-Ayala, Daniel J M, Guerra, Ignacio, Jiménez-Gancedo, Sandra, Cascajo, Maria V, Gavilán, Angela, DiMauro, Salvatore, Hirano, Michio, Briones, Paz, Artuch, Rafael, De Cabo, Rafael, Salviati, Leonardo, Navas, Plácido

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Secondary CoQ10 deficiency, bioenergetics unbalance in disease and aging von Navas, Plácido, Cascajo, María V., Alcázar‐Fabra, María, Hernández‐Camacho, Juan D., Sánchez‐Cuesta, Ana, Rodríguez, Ana Belén Cortés, Ballesteros‐Simarro, Manuel, Arroyo‐Luque, Antonio, Rodríguez‐Aguilera, Juan Carlos, Fernández‐Ayala, Daniel J. M., Brea‐Calvo, Gloria, López‐Lluch, Guillermo, Santos‐Ocaña, Carlos

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Secondary CoQ 10 deficiency, bioenergetics unbalance in disease and aging von Navas, Plácido, Cascajo, María V, Alcázar-Fabra, María, Hernández-Camacho, Juan D, Sánchez-Cuesta, Ana, Rodríguez, Ana Belén Cortés, Ballesteros-Simarro, Manuel, Arroyo-Luque, Antonio, Rodríguez-Aguilera, Juan Carlos, Fernández-Ayala, Daniel J M, Brea-Calvo, Gloria, López-Lluch, Guillermo, Santos-Ocaña, Carlos

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ADCK2 Haploinsufficiency Reduces Mitochondrial Lipid Oxidation and Causes Myopathy Associated with CoQ Deficiency von Vázquez-Fonseca, Luis, Schaefer, Jochen, Navas-Enamorado, Ignacio, Santos-Ocaña, Carlos, Hernández-Camacho, Juan D, Guerra, Ignacio, Cascajo, María V, Sánchez-Cuesta, Ana, Horvath, Zoltan, Siendones, Emilio, Jou, Cristina, Casado, Mercedes, Gutiérrez, Purificación, Brea-Calvo, Gloria, López-Lluch, Guillermo, Fernández-Ayala, Daniel J M, Cortés-Rodríguez, Ana B, Rodríguez-Aguilera, Juan C, Matté, Cristiane, Ribes, Antonia, Prieto-Soler, Sandra Y, Dominguez-Del-Toro, Eduardo, Francesco, Andrea di, Aon, Miguel A, Bernier, Michel, Salviati, Leonardo, Artuch, Rafael, Cabo, Rafael de, Jackson, Sandra, Navas, Plácido

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Laboratory Diagnosis of a Case with Coenzyme Q(10) Deficiency von Paredes-Fuentes, Abraham J., Julia-Palacios, Natalia A., Montero, Raquel, Yubero, Delia, Cascajo-Almenara, Maria V., Garcia-Cazorla, Angels, Santos-Ocana, Carlos, Artuch, Rafael

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Laboratory Diagnosis of a Case with Coenzyme [Q.sub.10] Deficiency von Paredes-Fuentes, Abraham J, Julia-Palacios, Natalia A, Montero, Raquel, Yubero, Delia, Cascajo-Almenara, Maria V, Garcia-Cazorla, Angels, Santos-Ocana, Carlos, Artucha, Rafael

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Survival transcriptome in the coenzyme Q 10 deficiency syndrome is acquired by epigenetic modifications: a modelling study for human coenzyme Q 10 deficiencies von Fernández-Ayala, Daniel J M, Guerra, Ignacio, Jiménez-Gancedo, Sandra, Cascajo, Maria V, Gavilán, Angela, DiMauro, Salvatore, Hirano, Michio, Briones, Paz, Artuch, Rafael, De Cabo, Rafael, Salviati, Leonardo, Navas, Plácido

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Laboratory Diagnosis of a Case with Coenzyme Q10 Deficiency von Paredes-Fuentes, Abraham J, Julià-Palacios, Natalia A, Montero, Raquel, Yubero, Dèlia, Cascajo-Almenara, María V, García-Cazorla, Àngels, Santos-Ocaña, Carlos, Artuch, Rafael

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Cardiac and placental mitochondrial characterization in a rabbit model of intrauterine growth restriction von Guitart-Mampel, M., Gonzalez-Tendero, A., Niñerola, S., Morén, C., Catalán-Garcia, M., González-Casacuberta, I., Juárez-Flores, D.L., Ugarteburu, O., Matalonga, L., Cascajo, M.V., Tort, F., Cortés, A., Tobias, E., Milisenda, J.C., Grau, J.M., Crispi, F., Gratacós, E., Garrabou, G., Cardellach, F.

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Brain organoid as a model to study the role of mitochondria in neurodevelopmental disorders: achievements and weaknesses von Coronel, Raquel, García-Moreno, Enrique, Siendones, Emilio, Barrero, Maria J, Martínez-Delgado, Beatriz, Santos-Ocaña, Carlos, Liste, Isabel, Cascajo-Almenara, M V

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Mutations of GEMIN5 are associated with coenzyme Q10 deficiency: long-term follow-up after treatment von Cascajo-Almenara, Marivi V., Juliá-Palacios, Natalia, Urreizti, Roser, Sánchez-Cuesta, Ana, Fernández-Ayala, Daniel M., García-Díaz, Elena, Oliva, Clara, O´Callaghan, Maria del Mar, Paredes-Fuentes, Abraham J., Moreno-Lozano, Pedro J., Muchart, Jordi, Nascimento, Andres, Ortez, Carlos I., Natera-de Benito, Daniel, Pineda, Mercedes, Rivera, Noelia, Fortuna, Tyler R., Rajan, Deepa S., Navas, Plácido, Salviati, Leonardo, Palau, Francesc, Yubero, Delia, García-Cazorla, Angels, Pandey, Udai Bhan, Santos-Ocaña, Carlos, Artuch, Rafael

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Development of the DRoplet Ice Nuclei Counter Zurich (DRINCZ): validation and application to field-collected snow samples von David, Robert O, Cascajo-Castresana, Maria, Brennan, Killian P, Rösch, Michael, Els, Nora, Werz, Julia, Weichlinger, Vera, Boynton, Lin S, Bogler, Sophie, Borduas-Dedekind, Nadine, Marcolli, Claudia, Kanji, Zamin A

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Mutations of GEMIN5 are associated with coenzyme Q 10 deficiency: long-term follow-up after treatment von Cascajo-Almenara, Marivi V, Juliá-Palacios, Natalia, Urreizti, Roser, Sánchez-Cuesta, Ana, Fernández-Ayala, Daniel M, García-Díaz, Elena, Oliva, Clara, O Callaghan, Maria Del Mar, Paredes-Fuentes, Abraham J, Moreno-Lozano, Pedro J, Muchart, Jordi, Nascimento, Andres, Ortez, Carlos I, Natera-de Benito, Daniel, Pineda, Mercedes, Rivera, Noelia, Fortuna, Tyler R, Rajan, Deepa S, Navas, Plácido, Salviati, Leonardo, Palau, Francesc, Yubero, Delia, García-Cazorla, Angels, Pandey, Udai Bhan, Santos-Ocaña, Carlos, Artuch, Rafael

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Cardiac and placental mitochondrial characterization in a rabbit model of intrauterine growth restriction von Guitart Mampel, Mariona, Gonzalez-Tendero, Anna, Niñerola, S, Morén Núñez, Constanza, Catalán García, Marc, González-Casacuberta, I, Juárez Flores, Diana Luz, Ugarteburu, O, Matalonga, L, Cascajo, M. V, Tort, F, Cortés, A, Tobias, E, Milisenda, José, Grau Junyent, Josep M. (Josep Maria), Crispi Brillas, Fàtima, Gratacós Solsona, Eduard, Garrabou Tornos, Glòria, Cardellach, Francesc

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Cardiac and placental mitochondrial characterization in a rabbit model of intrauterine growth restriction von Guitart Mampel, Mariona, González Tendero, Anna, Niñerola, S, Morén Núñez, Constanza, Catalán García, Marc, González Casacuberta, Ingrid, Juárez Flores, Diana Luz, Ugarteburu López, Olatz, Matalonga Borrel, Lesley, Cascajo, M. V, Tort, Frederic, Cortés, A, Tobías, Ester, Milisenda, José, Grau Junyent, Josep M. (Josep Maria), Crispi Brillas, Fàtima, Gratacós Solsona, Eduard, Garrabou Tornos, Glòria, Cardellach, Francesc

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