Mutations at the Lysosomal Acid Cholesteryl Ester Hydrolase Gene Locus in Wolman Disease von Anderson, Richard A., Byrum, Robert S., Coates, Paul M., Sando, Gloria N.

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The development and implementation of quality assurance programs to support nutritional measurements von Sander, L. C., Bedner, M., Duewer, D. L., Lippa, K. A., Phillips, M. M., Phinney, K. W., Rimmer, C. A., Schantz, M. M., Sharpless, K. E., Tai, S. S. -C., Thomas, J. B., Wise, S. A., Wood, L. J., Betz, J. M., Coates, P. M.

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Molecular basis of mitochondrial fatty acid oxidation defects von Coates, PM, Tanaka, K

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Chronic cardiomyopathy and weakness or acute coma in children with a defect in carnitine uptake von Stanley, Charles A., DeLeeuw, Susan, Coates, Paul M., Vianey-Liaud, Christine, Divry, Priscille, Bonnefont, Jean-Paul, Saudubray, Jean-Marie, Haymond, Morey, Trefz, Friedrich K., Breningstall, Galen N., Wappner, Rebecca S., Byrd, Dennis J., Sansaricq, Claude, Tein, Ingrid, Grover, Warren, Valle, David, Rutledge, S. Lane, Treem, William R.

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A 5' splice-region mutation and a dinucleotide deletion in the lysosomal acid lipase gene in two patients with cholesteryl ester storage disease von Ameis, D, Brockmann, G, Knoblich, R, Merkel, M, Ostlund, R E, Yang, J W, Coates, P M, Cortner, J A, Feinman, S V, Greten, H

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Very-long-chain acyl-CoA dehydrogenase deficiency: molecular genetics of a mitochondrial membrane enzyme von Coates, P M

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Effects of family history of heart disease, apolipoprotein E phenotype, and lipoprotein(a) on the response of children’s plasma lipids to change in dietary lipids von Dixon, LB, Shannon, BM, Tershakovec, AM, Bennett, MJ, Coates, PM, Cortner, JA

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Kinetics of chylomicron remnant clearance in normal and in hyperlipoproteinemic subjects von Cortner, J A, Coates, P M, Le, N A, Cryer, D R, Ragni, M C, Faulkner, A, Langer, T

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Familial combined hyperlipidaemia: Use of stable isotopes to demonstrate overproduction of very low‐density lipoprotein apolipoprotein B by the liver von Cortner, J. A., Coates, P. M., Bennett, M. J., Cryer, D. R., Le, Ngoc‐Anh

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Identification of very-long-chain acyl-CoA dehydrogenase deficiency in three patients previously diagnosed with long-chain acyl-CoA dehydrogenase deficiency von YAMAGUCHI, S, INDO, Y, COATES, P. M, HASHIMOTO, T, TANAKA, K

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Genetic deficiency of short-chain acyl-coenzyme A dehydrogenase in cultured fibroblasts from a patient with muscle carnitine deficiency and severe skeletal muscle weakness von COATES, P. M, HALE, D. E, FINOCCHIARO, G, TANAKA, K, WINTER, S. C

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Relationship between unusual hepatic acyl coenzyme A profiles and the pathogenesis of Reye syndrome von CORKEY, B. E, HALE, D. E, GLENNON, M. C, KELLEY, R. I, COATES, P. M, KILPATRICK, L, STANLEY, C. A

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Familial combined hyperlipidemia in children: Clinical expression, metabolic defects, and management von Cortner, Jean A., Coates, Paul M., Liacouras, Chris A., Jarvik, Gall P.

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Mutations in the medium chain acyl-CoA dehydrogenase (MCAD) gene von Tanaka, K., Yokota, I., Coates, P. M., Strauss, A. W., Kelly, D. P., Zhang, Z., Gregersen, N., Andresen, B. S., Matsubara, Y., Curtis, D., Chen, Y.-T.

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Kinetics of retinyl esters during postprandial lipemia in man: A compartmental model von Le, Ngoc-Anh, Coates, Paul M., Gallagher, Paul R., Cortner, Jean A.

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Long-chain acyl coenzyme A dehydrogenase deficiency: an inherited cause of nonketotic hypoglycemia von HALE, D. E, BATSHAW, M. L, COATES, P. M, FRERMAN, F. E, GOODMAN, S. I, INDERJIT SINGH, STANLEY, C. A

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Use of cholestyramine in the treatment of children with familial combined hyperlipidemia von Liacouras, Chris A., Coates, Paul M., Gallagher, Paul R., Cortner, Jean A.

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Genetic deficiency of medium-chain acyl coenzyme A dehydrogenase: studies in cultured skin fibroblasts and peripheral mononuclear leukocytes von COATES, P. M, HALE, D. E, STANLEY, C. A, CORKEY, B. E, CORTNER, J. A

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Primary Carnitine Deficiency Due to a Failure of Carnitine Transport in Kidney, Muscle, and Fibroblasts von Treem, William R, Stanley, Charles A, Finegold, David N, Hale, Daniel E, Coates, Paul M

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Evidence-Based Reviews in Support of Health Policy Decisions von Coates, Paul M.

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