Mitochondrial disorders and general anaesthesia: a case series and review von Footitt, E.J., Sinha, M.D., Raiman, J.A.J., Dhawan, A., Moganasundram, S., Champion, M.P.

Volltext

Hepatocyte Transplantation Followed by Auxiliary Liver Transplantation—a Novel Treatment for Ornithine Transcarbamylase Deficiency von Puppi, J., Tan, N., Mitry, R. R., Hughes, R. D., Lehec, S., Mieli‐Vergani, G., Karani, J., Champion, M. P., Heaton, N., Mohamed, R., Dhawan, A.

Volltext

novel starch for the treatment of glycogen storage diseases von Bhattacharya, K, Orton, R. C, Qi, X, Mundy, H, Morley, D. W, Champion, M. P, Eaton, S, Tester, R. F, Lee, P. J

Volltext

Nuclear resonance vibrational spectroscopy of a protein active-site mimic von Sage, J T, Paxson, C, Wyllie, G R A, Sturhahn, W, Durbin, S M, Champion, P M, Alp, E E, Scheidt, W R

Volltext

An approach to the diagnosis of inherited metabolic disease von Champion, MP

Volltext

High frequency of missense mutations in glycogen storage disease type VI von Beauchamp, N. J, Taybert, J, Champion, M. P, Layet, V, Heinz-Erian, P, Dalton, A, Tanner, M. S, Pronicka, E, Sharrard, M. J

Volltext

Refining the diagnosis of mitochondrial HMG‐CoA synthase deficiency von Aledo, R., Mir, C., Dalton, R. N., Turner, C., Pié, J., Hegardt, F. G., Casals, N., Champion, M. P.

Volltext

Clinical, enzymatic and molecular characterization of nine new patients with malonyl‐coenzyme A decarboxylase deficiency von Salomons, G. S., Jakobs, C., Pope, L. Landegge, Errami, A., Potter, M., Nowaczyk, M., Olpin, S., Manning, N., Raiman, J. A. J., Slade, T., Champion, M. P., Peck, D., Gavrilov, D., Hillman, R., Hoganson, G. E., Donaldson, K., Shield, J. P. H., Ketteridge, D., Wasserstein, M., Gibson, K. M.

Volltext

Biotinidase Deficiency: a Treatable Leukoencephalopathy von Grünewald, S., Champion, M. P., Leonard, J. V., Schaper, J., Morris, A. A. M.

Volltext

Serum lactate as a predictor of mortality after paediatric cardiac surgery von Hatherill, M, Sajjanhar, T, Tibby, S M, Champion, M P, Anderson, D, Marsh, M J, Murdoch, I A

Volltext

Outcome of medium chain acyl-CoA dehydrogenase deficiency after diagnosis von Wilson, Callum J, Champion, Michael P, Collins, Jane E, Clayton, Peter T, Leonard, James V

Volltext

Duodenal perforation: a diagnostic pitfall in non-accidental injury von Champion, M P, Richards, C A, Boddy, S A, Ward, H C

Volltext

How reliable is the allopurinol load in detecting carriers for ornithine transcarbamylase deficiency? von Grünewald, S., Fairbanks, L., Genet, S., Cranston, T., Hüsing, J., Leonard, J. V., Champion, M. P.

Volltext

Investigations of Ligand Association and Dissociation Rates in the "Open" and "Closed" States of Myoglobin von Tian, W.D., Sage, J.T., Champion, P.M.

Volltext

Protein fluctuations, distributed coupling, and the binding of ligands to heme proteins von Srajer, V, Reinisch, L, Champion, P. M

Volltext

RELAXATION DYNAMICS OF MYOGLOBIN IN SOLUTION von TIAN, WD, SAGE, JT, SRAJER, CHAMPION, PM

Volltext

The Birth Prevalence of PKU in Populations of European, South Asian and Sub‐Saharan African Ancestry Living in South East England von Hardelid, P., Cortina‐Borja, M., Munro, A., Jones, H., Cleary, M., Champion, M. P., Foo, Y., Scriver, C. R., Dezateux, C.

Volltext

Spectroscopic Effects of Polarity and Hydration in the Distal Heme Pocket of Deoxymyoglobin von Christian, J. F, Unno, M, Sage, J. T, Champion, P. M, Chien, E, Sligar, S. G

Volltext

Spectroscopic studies of myoglobin at low pH: heme structure and ligation von Sage, J. Timothy, Morikis, Dimitrios, Champion, Paul M

Volltext

Raman and kinetic studies of myoglobin structure and dynamics von Champion, P. M.

Volltext