Inhibition of histone deacetylase 6 activity reduces cyst growth in polycystic kidney disease von Cebotaru, Liudmila, Liu, Qiangni, Yanda, Murali K., Boinot, Clement, Outeda, Patricia, Huso, David L., Watnick, Terry, Guggino, William B., Cebotaru, Valeriu

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Combination of Correctors Rescues CFTR Transmembrane-Domain Mutants by Mitigating their Interactions with Proteostasis von Lopes-Pacheco, Miquéias, Boinot, Clément, Sabirzhanova, Inna, Rapino, Daniele, Cebotaru, Liudmila

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Rescue of NBD2 mutants N1303K and S1235R of CFTR by small-molecule correctors and transcomplementation von Rapino, Daniele, Sabirzhanova, Inna, Lopes-Pacheco, Miquéias, Grover, Rahul, Guggino, William B, Cebotaru, Liudmila

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Syntaxin 6 and CAL mediate the degradation of the cystic fibrosis transmembrane conductance regulator von Cheng, Jie, Cebotaru, Valeriu, Cebotaru, Liudmila, Guggino, William B

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The CFTR Corrector, VX-809 (Lumacaftor), Rescues ABCA4 Trafficking Mutants: a Potential Treatment for Stargardt Disease von Liu, Qiangni, Sabirzhanova, Inna, Bergbower, Emily Anne Smith, Yanda, Murali, Guggino, William G, Cebotaru, Liudmila

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CFTR Modulators Mitigate Autosomal Recessive Polycystic Kidney Disease: SA-PO781 von Ciobanu, Cristian, Cebotaru, Liudmila

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Correcting the cystic fibrosis disease mutant, A455E CFTR von Cebotaru, Liudmila, Rapino, Daniele, Cebotaru, Valeriu, Guggino, William B

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The CFTR-Associated Ligand Arrests the Trafficking of the Mutant ΔF508 CFTR Channel in the ER Contributing to Cystic Fibrosis von Bergbower, Emily, Boinot, Clement, Sabirzhanova, Inna, Guggino, William, Cebotaru, Liudmila

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Syntaxin 8 and the Endoplasmic Reticulum Processing of ΔF508-CFTR von Sabirzhanova, Inna, Boinot, Clément, Guggino, William B., Cebotaru, Liudmila

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WNK4 Enhances the Degradation of NCC through a Sortilin-Mediated Lysosomal Pathway von BO ZHOU, JIEQIU ZHUANG, DINGYING GU, HUA WANG, CEBOTARU, Liudmila, GUGGINO, William B, HUI CAI

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CFTR Controls the Activity of NF-κB by Enhancing the Degradation of TRADD von Wang, Hua, Cebotaru, Liudmila, Lee, Ha Won, Yang, QingFeng, Pollard, Bette S., Pollard, Harvey B., Guggino, William B.

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Restoration of F508-del Function by Transcomplementation: The Partners Meet in the Endoplasmic Reticulum von Bergbower, Emily Anne Smith, Sabirzhanova, Inna, Boinot, Clément, Guggino, William B, Cebotaru, Liudmila

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Dexamethasone regulates CFTR expression in Calu-3 cells with the involvement of chaperones HSP70 and HSP90 von Prota, Luiz Felipe M, Cebotaru, Liudmila, Cheng, Jie, Wright, Jerry, Vij, Neeraj, Morales, Marcelo M, Guggino, William B

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Enterohemorrhagic Escherichia coli infection stimulates Shiga toxin 1 macropinocytosis and transcytosis across intestinal epithelial cells von Lukyanenko, Valeriy, Malyukova, Irina, Hubbard, Ann, Delannoy, Michael, Boedeker, Edgar, Zhu, Chengru, Cebotaru, Liudmila, Kovbasnjuk, Olga

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Treatment of Autosomal Recessive Polycystic Kidney Disease With CFTR Modulators: TH-PO414 von Cebotaru, Liudmila, Yanda, Murali K.

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Role of CFTR in Autosomal Dominant Polycystic Kidney Disease: FR-PO272 von Cebotaru, Liudmila, Yanda, Murali K.

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Therapeutic Potential of a CFTR Corrector to Mitigate Slowly Progressing Adult-Onset Polycystic Kidney Disease: TH-OR36 von Cebotaru, Liudmila, Yanda, Murali K.

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STIM1fl/fl Ksp-Cre Mouse has Impaired Renal Water Balance von Cebotaru, Liudmila, Cebotaru, Valeriu, Wang, Hua, Arend, Lois J., Guggino, William B.

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Dual Reporter Comparative Indexing of rAAV Pseudotyped Vectors in Chimpanzee Airway von Flotte, Terence R, Fischer, Anne C, Goetzmann, Jason, Mueller, Christian, Cebotaru, Liudmila, Yan, Ziying, Wang, Lilli, Wilson, James M, Guggino, William B, Engelhardt, John F

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Regulation of CFTR Expression and Arginine Vasopressin Activity Are Dependent on Polycystin-1 in Kidney-Derived Cells von de Lemos Barbosa, Carolina Monteiro, Souza-Menezes, Jackson, Amaral, Andressa Godoy, Onuchic, Luiz Fernando, Cebotaru, Liudmila, Guggino, William B., Morales, Marcelo M.

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