Central nervous system inflammation is a hallmark of pathogenesis in mouse models of GM1 and GM2 gangliosidosis von Jeyakumar, M., Thomas, R., Elliot‐Smith, E., Smith, D. A., van der Spoel, A. C., d’Azzo, A., Hugh Perry, V., Butters, T. D., Dwek, R. A., Platt, F. M.

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Sustained therapeutic effects of oral miglustat (Zavesca, N‐butyldeoxynojirimycin, OGT 918) in type I Gaucher disease von Elstein, D., Hollak, C., Aerts, J. M. F. G., Weely, S., Maas, M., Cox, T. M., Lachmann, R. H., Hrebicek, M., Platt, F. M., Butters, T. D., Dwek, R. A., Zimran, A.

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Serum glycomarkers of endoplasmic reticulum and lysosomal-endosomal system stress in human healthy aging and diseases von Pismenetskaya, I U, Butters, T D

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Glycosphingolipid lysosomal storage diseases: therapy and pathogenesis von Jeyakumar, M., Butters, T. D., Dwek, R. A., Platt, F. M.

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Heart failure in a woman with SLE, anti-phospholipid syndrome and Fabry’s disease von Nandagudi, A, Jury, EC, Alonzi, D, Butters, TD, Hughes, S, Isenberg, DA

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N-butyldeoxynojirimycin is a novel inhibitor of glycolipid biosynthesis von PLATT, F. M, NEISES, G. R, DWEK, R. A, BUTTERS, T. D

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Study of the Mechanism of Antiviral Action of Iminosugar Derivatives against Bovine Viral Diarrhea Virus von Durantel, D, Branza-Nichita, N, Carrouée-Durantel, S, Butters, T D, Dwek, R A, Zitzmann, N

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Severe endothelial dysfunction in the aorta of a mouse model of Fabry disease; partial prevention by N‐butyldeoxynojirimycin treatment von Heare, T., Alp, N. J., Priestman, D. A., Kulkarni, A. B., Qasba, P., Butters, T. D., Dwek, R. A., Clarke, K., Channon, K. M., Platt, F. M.

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Inhibition of substrate synthesis as a strategy for glycolipid lysosomal storage disease therapy von Platt, F. M., Jeyakumar, M., Andersson, U., Priestman, D. A., Dwek, R. A., Butters, T. D., Cox, T. M., Lachmann, R. H., Hollak, C., Aerts, J. M. F. G., Van Weely, S., Hrebícek, M., Moyses, C., Gow, I., Elstein, D., Zimran, A.

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N-butyldeoxynojirimycin causes weight loss as a result of appetite suppression in lean and obese mice von Priestman, D.A, van der Spoel, A.C, Butters, T.D, Dwek, R.A, Platt, F.M

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Prevention of Lysosomal Storage in Tay-Sachs Mice Treated with N-Butyldeoxynojirimycin von Platt, Frances M., Neises, Gabrielle R., Reinkensmeier, Gabriele, Townsend, Mandy J., Perry, V. Hugh, Proia, Richard L., Winchester, Bryan, Dwek, Raymond A., Butters, Terry D.

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N-butyldeoxygalactonojirimycin: a more selective inhibitor of glycosphingolipid biosynthesis than N-butyldeoxynojirimycin, in vitro and in vivo von Andersson, Ulrika, Butters, Terry D, Dwek, Raymond A, Platt, Frances M

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New therapeutic prospects for the glycosphingolipid lysosomal storage diseases von PLATT, F. M, BUTTERS, T. D

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The alpha-glucosidase inhibitor N-butyldeoxynojirimycin inhibits human immunodeficiency virus entry at the level of post-CD4 binding von Fischer, P B, Collin, M, Karlsson, G B, James, W, Butters, T D, Davis, S J, Gordon, S, Dwek, R A, Platt, F M

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N-butyldeoxynojirimycin-mediated inhibition of human immunodeficiency virus entry correlates with changes in antibody recognition of the V1/V2 region of gp120 von Fischer, P B, Karlsson, G B, Butters, T D, Dwek, R A, Platt, F M

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Novel imino sugar α-glucosidase inhibitors as antiviral compounds von Howe, J.D., Smith, N., Lee, M.J.-R., Ardes-Guisot, N., Vauzeilles, B., Désiré, J., Baron, A., Blériot, Y., Sollogoub, M., Alonzi, D.S., Butters, T.D.

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N- and C-alkylation of seven-membered iminosugars generates potent glucocerebrosidase inhibitors and F508del-CFTR correctors von Désiré, J, Mondon, M, Fontelle, N, Nakagawa, S, Hirokami, Y, Adachi, I, Iwaki, R, Fleet, G W J, Alonzi, D S, Twigg, G, Butters, T D, Bertrand, J, Cendret, V, Becq, F, Norez, C, Marrot, J, Kato, A, Blériot, Y

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Structural essentials for β-N-acetylhexosaminidase inhibition by amides of prolines, pipecolic and azetidine carboxylic acids von Glawar, A F G, Martínez, R F, Ayers, B J, Hollas, M A, Ngo, N, Nakagawa, S, Kato, A, Butters, T D, Fleet, G W J, Jenkinson, S F

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Effects of the imino sugar N-butyldeoxynojirimycin on the N-glycosylation of recombinant gp120 von KARLSSON, G. B, BUTTERS, T. D, DWEK, R. A, PLATT, F. M

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High-Performance Liquid Chromatography Analysis of Ganglioside Carbohydrates at the Picomole Level after Ceramide Glycanase Digestion and Fluorescent Labeling with 2-Aminobenzamide von Wing, D.R., Garner, B., Hunnam, V., Reinkensmeier, G., Andersson, U., Harvey, D.J., Dwek, R.A., Platt, F.M., Butters, T.D.

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