Neuroprotective Effects of Phenylbutyrate in the N171-82Q Transgenic Mouse Model of Huntington's Disease von Gardian, Gabriella, Browne, Susan E., Choi, Dong-Kug, Klivenyi, Peter, Gregorio, Jason, Kubilus, James K., Ryu, Hoon, Langley, Brett, Ratan, Rajiv R., Ferrante, Robert J., Beal, M. Flint

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Mitochondria and Huntington's disease pathogenesis: insight from genetic and chemical models von Browne, Susan E

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pivotal role of matrix metalloproteinase-3 activity in dopaminergic neuronal degeneration via microglial activation von Kim, Yoon Seong, Choi, Dong Hee, Block, Michelle L, Lorenzl, Stefan, Yang, Lichuan, Kim, Youn Jung, Sugama, Shuei, Cho, Byung Pil, Hwang, Onyou, Browne, Susan E, Kim, Soo Yul, Hong, Jau-Shyong, Beal, M. Flint, Joh, Tong H

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Bioenergetic abnormalities in discrete cerebral motor pathways presage spinal cord pathology in the G93A SOD1 mouse model of ALS von Browne, Susan E., Yang, Lichuan, DiMauro, Jon-Paul, Fuller, Sara W., Licata, Stephanie C., Beal, M. Flint

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Mitochondria and Huntington's Disease Pathogenesis von Browne, Susan E.

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Minocycline enhances MPTP toxicity to dopaminergic neurons von Yang, Lichuan, Sugama, Shuei, Chirichigno, Jason W., Gregorio, Jason, Lorenzl, Stefan, Shin, Dong H., Browne, Susan E., Shimizu, Yoshinori, Joh, Tong H., Beal, M. Flint, Albers, David S.

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Creatine Increases Survival and Delays Motor Symptoms in a Transgenic Animal Model of Huntington's Disease von Andreassen, Ole A., Dedeoglu, Alpaslan, Ferrante, Robert J., Jenkins, Bruce G., Ferrante, Kimberly L., Thomas, Melissa, Friedlich, Avi, Browne, Susan E., Schilling, Gabriele, Borchelt, David R., Hersch, Steven M., Ross, Christopher A., Beal, M.Flint

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When too much ATP is a bad thing: a pivotal role for P2X7 receptors in motor neuron degeneration von Browne, Susan E.

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Dual orexin receptor antagonists show distinct effects on locomotor performance, ethanol interaction and sleep architecture relative to gamma-aminobutyric acid-A receptor modulator... von Ramirez, Andres D, Gotter, Anthony L, Fox, Steven V, Tannenbaum, Pamela L, Yao, Lihang, Tye, Spencer J, McDonald, Terrence, Brunner, Joseph, Garson, Susan L, Reiss, Duane R, Kuduk, Scott D, Coleman, Paul J, Uslaner, Jason M, Hodgson, Robert, Browne, Susan E, Renger, John J, Winrow, Christopher J

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Mitochondrial alpha-ketoglutarate dehydrogenase complex generates reactive oxygen species von Starkov, Anatoly A, Fiskum, Gary, Chinopoulos, Christos, Lorenzo, Beverly J, Browne, Susan E, Patel, Mulchand S, Beal, M Flint

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A potent and selective metabotropic glutamate receptor 4 positive allosteric modulator improves movement in rodent models of Parkinson's disease von Le Poul, Emmanuel, Boléa, Christelle, Girard, Francoise, Poli, Sonia, Charvin, Delphine, Campo, Brice, Bortoli, Julien, Bessif, Abdhelak, Luo, Bin, Koser, Amy Jo, Hodge, Lisa M, Smith, Karen M, DiLella, Anthony G, Liverton, Nigel, Hess, Fred, Browne, Susan E, Reynolds, Ian J

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Characterization of the novel positive allosteric modulator of the metabotropic glutamate receptor 4 ADX88178 in rodent models of neuropsychiatric disorders von Kalinichev, Mikhail, Le Poul, Emmanuel, Boléa, Christelle, Girard, Françoise, Campo, Brice, Fonsi, Massimiliano, Royer-Urios, Isabelle, Browne, Susan E, Uslaner, Jason M, Davis, Matthew J, Raber, Jacob, Duvoisin, Robert, Bate, Simon T, Reynolds, Ian J, Poli, Sonia, Celanire, Sylvain

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Huntington's Disease of the Endocrine Pancreas: Insulin Deficiency and Diabetes Mellitus due to Impaired Insulin Gene Expression von Andreassen, Ole A., Dedeoglu, Alpaslan, Stanojevic, Violeta, Hughes, Duncan B., Browne, Susan E., Leech, Colin A., Ferrante, Robert J., Habener, Joel F., Beal, M.Flint, Thomas, Melissa K.

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CHIP and Hsp70 regulate tau ubiquitination, degradation and aggregation von Petrucelli, Leonard, Dickson, Dennis, Kehoe, Kathryn, Taylor, Julie, Snyder, Heather, Grover, Andrew, De Lucia, Michael, McGowan, Eileen, Lewis, Jada, Prihar, Guy, Kim, Jungsu, Dillmann, Wolfgang H., Browne, Susan E., Hall, Alexis, Voellmy, Richard, Tsuboi, Yoshio, Dawson, Ted M., Wolozin, Benjamin, Hardy, John, Hutton, Mike

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The energetics of Huntington's disease von Browne, Susan E, Beal, M Flint

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Validation of high-sensitivity assays to quantitate cerebrospinal fluid and serum β-galactosidase activity in patients with GM1-gangliosidosis von Quadrini, Karen J., Vrentas, Catherine, Duke, Christian, Wilson, Chris, Hinderer, Christian J., Weinstein, David A., Al-Zaidy, Samiah A., Browne, Susan E., Wilson, James M., Ni, Yan G.

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Oral uridine pro-drug PN401 is neuroprotective in the R6/2 and N171-82Q mouse models of Huntington's disease von Saydoff, Joel A., Garcia, Rolando A.G., Browne, Susan E., Liu, Liansheng, Sheng, Jin, Brenneman, Denise, Hu, Zhongyi, Cardin, Sylvain, Gonzalez, Alexis, von Borstel, Reid W., Gregorio, Jason, Burr, Holly, Beal, M. Flint

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Oxidative Stress in Huntington's Disease von Browne, Susan E., Ferrante, Robert J., Beal, M. Flint

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Oxidative damage and metabolic dysfunction in Huntington's disease: Selective vulnerability of the basal ganglia von Browne, Susan E., Bowling, Allen C., Macgarvey, Usha, Baik, M. Jay, Berger, Stephanie C., Muquit, Miratul M. K., Bird, Edward D., Beal, M. Flint

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Increased 3-nitrotyrosine in both sporadic and familial amyotrophic lateral sclerosis von Beal, M. Flint, Ferrante, Robert J., Browne, Susan E., Matthews, Russell T., Kowall, Neil W., Brown Jr, Robert H.

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