Misleading Clinical Symptoms and a Prolonged Diagnostic Approach in Prepyloric Web von Vries, AGM, Bodewes, FAJA, Baren, R, Karrenbeld, A, Broens, PMA

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Ursodeoxycholate modulates bile flow and bile salt pool independently from the cystic fibrosis transmembrane regulator (Cftr) in mice von Bodewes, Frank A J A, Wouthuyzen-Bakker, Marjan, Bijvelds, Marcel J, Havinga, Rick, de Jonge, Hugo R, Verkade, Henkjan J

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Cystic Fibrosis Related Liver Disease: Research Challenges and Future Perspectives von Debray, Dominique, Narkewicz, Michael R, Bodewes, Frank A.J.A, Colombo, Carla, Housset, Chantal, de Jonge, Hugo R, Jonker, Johan W, Kelly, Deirdre A, Ling, Simon C, Poynard, Thierry, Sogni, Philippe, Trauner, Michael, Witters, Peter, Baumann, Ulrich, Wilschanski, Michael, Verkade, Henkjan J

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Rationale and design of TransplantLines: a prospective cohort study and biobank of solid organ transplant recipients von Eisenga, Michele F, Gomes-Neto, Antonio W, van Londen, Marco, Ziengs, Aaltje L, Douwes, Rianne M, Stam, Suzanne P, Osté, Maryse C J, Knobbe, Tim J, Hessels, Niek R, Buunk, Anne M, Annema, Coby, Siebelink, Marion J, Racz, Emoke, Spikman, Jacoba M, Bodewes, Frank A J A, Pol, Robert A, Berger, Stefan P, Drost, Gea, Porte, Robert J, Leuvenink, Henri G D, Damman, Kevin, Verschuuren, Erik A M, de Meijer, Vincent E, Blokzijl, Hans, Bakker, Stephan J L

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Towards a Standardized Classification of the Hepatobiliary Manifestations in Cystic Fibrosis (CFHBI): A Joint ESPGHAN/NASPGHAN Position Paper von Bodewes, Frank A.J.A., Freeman, Alvin Jay, Weymann, Alexander, Debray, Dominique, Scheers, Isabelle, Verkade, Henkjan J., Narkewicz, Michael R.

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Diagnosis, follow-up and treatment of cystic fibrosis-related liver disease von van de Peppel, Ivo P, Bertolini, Anna, Jonker, Johan W, Bodewes, Frank A.J.A, Verkade, Henkjan J

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Cholic acid induces a Cftr dependent biliary secretion and liver growth response in mice von Bodewes, Frank A J A, Bijvelds, Marcel J, de Vries, Willemien, Baller, Juul F W, Gouw, Annette S H, de Jonge, Hugo R, Verkade, Henkjan J

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Bile acid homeostasis in gastrointestinal and metabolic complications of cystic fibrosis von van de Peppel, Ivo P., Bodewes, Frank A.J.A., Verkade, Henkjan J., Jonker, Johan W.

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IVACAFTOR restores FGF19 regulated bile acid homeostasis in cystic fibrosis patients with an S1251N or a G551D gating mutation von van de Peppel, Ivo P., Doktorova, Marcela, Berkers, Gitte, de Jonge, Hugo R., Houwen, Roderick H.J., Verkade, Henkjan J., Jonker, Johan W., Bodewes, Frank A.J.A.

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Defective FXR-FGF15 signaling and bile acid homeostasis in cystic fibrosis mice can be restored by the laxative polyethylene glycol von Bertolini, Anna, van de Peppel, Ivo P, Doktorova-Demmin, Marcela, Bodewes, Frank A J A, de Jonge, Hugo, Bijvelds, Marcel, Verkade, Henkjan J, Jonker, Johan W

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Gastroenterological endpoints in drug trials for cystic fibrosis von Bodewes, Frank A.J.A., Verkade, Henkjan J., Wilschanski, Micheal

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Altered intestinal bile salt biotransformation in a cystic fibrosis ( Cftr−/− ) mouse model with hepato-biliary pathology von Bodewes, Frank A.J.A, van der Wulp, Mariëtte Y.M, Beharry, Satti, Doktorova, Marcela, Havinga, Rick, Boverhof, Renze, James Phillips, M, Durie, Peter R, Verkade, Henkjan J

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ECFS standards of care on CFTR-related disorders: Identification and care of the disorders von Simmonds, N.J., Southern, K.W., De Wachter, E., De Boeck, K., Bodewes, F., Mainz, J.G., Middleton, P.G., Schwarz, C., Vloeberghs, V., Wilschanski, M., Bourrat, E., Chalmers, J.D., Ooi, C.Y., Debray, D., Downey, D.G., Eschenhagen, P., Girodon, E., Hickman, G., Koitschev, A., Nazareth, D., Nick, J.A., Peckham, D., VanDevanter, D., Raynal, C., Scheers, I., Waller, M.D., Sermet-Gaudelus, I., Castellani, C.

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Energy Balance and Mechanisms of Weight Gain with Ivacaftor Treatment of Cystic Fibrosis Gating Mutations von Stallings, Virginia A., Sainath, Nina, Oberle, Megan, Bertolaso, Chiara, Schall, Joan I.

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Hepatostat: Liver regeneration and normal liver tissue maintenance von Michalopoulos, George K.

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Cystic fibrosis transmembrane conductance regulator modulators and the exocrine pancreas: A scoping review von Ramsey, Mitchell L., Li, Susan S., Lara, Luis F., Gokun, Yevgeniya, Akshintala, Venkata S., Conwell, Darwin L., Heintz, John, Kirkby, Stephen E., McCoy, Karen S., Papachristou, Georgios I., Patel, Alpa, Singh, Vikesh K., Hart, Phil A.

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Cystic fibrosis hepatobiliary involvement: an update on imaging in diagnosis and monitoring von Wood, William, Tinich, Treiy, Lazar, Lauren, Schooler, Gary R., Sathe, Meghana

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Deleterious Variants in ABCC12 are Detected in Idiopathic Chronic Cholestasis and Cause Intrahepatic Bile Duct Loss in Model Organisms von Pham, Duc-Hung, Kudira, Ramesh, Xu, Lingfen, Valencia, C. Alexander, Ellis, Jillian L., Shi, Tiffany, Evason, Kimberley J., Osuji, Immaculeta, Matuschek, Nelson, Pfuhler, Liva, Mullen, Mary, Mohanty, Sujit K., Husami, Ammar, Bull, Laura N., Zhang, Kejian, Wali, Sami, Yin, Chunyue, Miethke, Alexander

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Impaired Intestinal Farnesoid X Receptor Signaling in Cystic Fibrosis Mice von Ikpa, Pauline T, Doktorova, Marcela, Meijsen, Kelly F, Nieuwenhuijze, Natascha D.A, Verkade, Henkjan J, Jonker, Johan W, de Jonge, Hugo R, Bijvelds, Marcel J.C

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Species differences in bile acids I. Plasma and urine bile acid composition von Thakare, Rhishikesh, Alamoudi, Jawaher Abdullah, Gautam, Nagsen, Rodrigues, A. David, Alnouti, Yazen

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