Deformation of Network Connectivity in the Inferior Olive of Connexin 36-Deficient Mice Is Compensated by Morphological and Electrophysiological Changes at the Single Neuron Level von De Zeeuw, Chris I, Chorev, Edilzh, Devor, Anna, Manor, Yait, Van Der Giessen, Ruben S, De Jeu, Marcel T, Hoogenraad, Casper C, Bijman, Jan, Ruigrok, Tom J. H, French, Pim, Jaarsma, Dick, Kistler, Werner M, Meier, Carola, Petrasch-Parwez, Elisabeth, Dermietzel, Rolf, Sohl, Goran, Gueldenagel, Martin, Willecke, Klaus, Yarom, Yosi

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Hearing loss in infantile Pompe's disease and determination of underlying pathology in the knockout mouse von Kamphoven, Joep H.J, de Ruiter, Martijn M, Winkel, Leon P.F, Van den Hout, Hannerieke M.P, Bijman, Jan, De Zeeuw, Chris I, Hoeve, Hans L, Van Zanten, Bert A, Van der Ploeg, Ans T, Reuser, Arnold J.J

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Isotype-specific Activation of Cystic Fibrosis Transmembrane Conductance Regulator-Chloride Channels by cGMP-dependent Protein Kinase II (∗) von French, Pim J., Bijman, Jan, Edixhoven, Marcel, Vaandrager, Arie B., Scholte, Bob J., Lohmann, Suzanne M., Nairn, Angus C., de Jonge, Hugo R.

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Chloride conductance and genetic background modulate the cystic fibrosis phenotype of Delta F508 homozygous twins and siblings von Bronsveld, I, Mekus, F, Bijman, J, Ballmann, M, de Jonge, H R, Laabs, U, Halley, D J, Ellemunter, H, Mastella, G, Thomas, S, Veeze, H J, Tümmler, B

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A mouse model for the cystic fibrosis delta F508 mutation von Doorninck, J. H., French, P. J., Verbeek, E., Peters, R. H., Morreau, H., Bijman, J., Scholte, B. J.

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Residual chloride secretion in intestinal tissue of ΔF508 homozygous twins and siblings with cystic fibrosis von Bronsveld, Inez, Mekus, Frauke, Bijman, Jan, Ballmann, Manfred, Greipel, Joachim, Hundrieser, Joachim, Halley, Dicky J.J., Laabs, Ulrike, Busche, Roger, De Jonge, Hugo R., Tümmler, Burkhard, Veeze, Henk J.

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A delta F508 mutation in mouse cystic fibrosis transmembrane conductance regulator results in a temperature-sensitive processing defect in vivo von French, P J, van Doorninck, J H, Peters, R H, Verbeek, E, Ameen, N A, Marino, C R, de Jonge, H R, Bijman, J, Scholte, B J

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Cystic fibrosis transmembrane conductance regulator (CFTR)-mediated residual chloride secretion does not protect against early chronic Pseudomonas aeruginosa infection in F508del h... von DERICHS, Nico, MEKUS, Frauke, BRONSVELD, Inez, BIJMAN, Jan, VEEZE, Henk J, VON DER HARDT, Horst, TÜMMLER, Burkhard, BALLMANN, Manfred

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Determinants of mild clinical symptoms in cystic fibrosis patients : residual chloride secretion measured in rectal biopsies in relation to the genotype von VEEZE, H. J, HALLEY, D. J. J, BIJMAN, J, DE JONGSTE, J. C, DE JONGE, H. R, SINAASAPPEL, M

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Cystic-fibrosis-like disease unrelated to the cystic fibrosis transmembrane conductance regulator von MEKUS, F, BALLMANN, M, BRONSVELD, I, DÖRK, T, BIJMAN, J, TÜMMLER, B, VEEZE, H. J

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Clinical presentation of exclusive cystic fibrosis lung disease von Bronsveld, Inez, Bijman, Jan, Mekus, Frauke, Ballmann, Manfred, Veeze, Henk J, Tümmler, Burkhard

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Ion transport abnormalities in rectal suction biopsies from children with cystic fibrosis von Veeze, Henk J., Sinaasappel, Maarten, Bijman, Jan, Bouquet, Jan, De Jonge, Hugo R.

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Cystic fibrosis transmembrane conductance regulator mediates the cyclic adenosine monophosphate‐induced fluid secretion but not the inhibition of resorption in mouse gallbladder ep... von Peters, R H, van Doorninck, J H, French, P J, Ratcliff, R, Evans, M J, Colledge, W H, Bijman, J, Scholte, B J

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Short Communications: Decreased C1 Permeability as the Basis for Increased Bioelectrical Potentials in Cvstic Fibrosis von Bijman, Jan

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G-proteins mediate intestinal chloride channel activation von TILLY, B. C, KANSEN, M, VAN GAGELDONK, P. G. M, VAN DEN BERGHE, N, GALJAARD, H, BIJMAN, J, DE JONGE, H. R

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CFTR expression and mucin secretion in cultured mouse gallbladder epithelial cells von Peters, R. H., French, P. J., van Doorninck, J. H., Lamblin, G., Ratcliff, R., Evans, M. J., Colledge, W. H., Bijman, J., Scholte, B. J.

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Permeability properties of cell membranes and tight junctions of normal and cystic fibrosis sweat ducts von BIJMAN, J, QUINTON, P

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Genistein activates CFTR Cl- channels via a tyrosine kinase- and protein phosphatase-independent mechanism von FRENCH, P. J, BIJMAN, J, BOT, A. G, BOOMAARS, W. E. M, SCHOLTE, B. J, DE JONGE, H. R

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Lactate and bicarbonate uptake in the sweat duct of cystic fibrosis and normal subjects von BIJMAN, J, QUINTON, P. M

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Immortalization of nasal polyp epithelial cells from cystic fibrosis patients von Scholte, Bob J., Kansen, Maarten, Hoogeveen, Andre T., Willemse, Rob, Rhim, Johng S., Van Der Kamp, Arthur W.M., Bijman, Jan

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