Genetic Risk Factors for Early-Onset Merkel Cell Carcinoma von Mohsin, Noreen, Hunt, Devin, Yan, Jia, Jabbour, Austin J, Nghiem, Paul, Choi, Jaehyuk, Zhang, Yue, Freeman, Alexandra F, Bergerson, Jenna R. E, Dell’Orso, Stefania, Lachance, Kristina, Kulikauskas, Rima, Collado, Loren, Cao, Wenjia, Lack, Justin, Similuk, Morgan, Seifert, Bryce A, Ghosh, Rajarshi, Walkiewicz, Magdalena A, Brownell, Isaac

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Warts and DADA2: a Mere Coincidence? von Arts, Katrijn, Bergerson, Jenna R. E., Ombrello, Amanda K., Similuk, Morgan, Oler, Andrew J., Agharahimi, Anahita, Mace, Emily M., Hershfield, Mike, Wouters, Carine, De Somer, Lien, Morren, Marie-Anne, Diego, Rebeca Perez-de, Moens, Leen, Freeman, Alexandra F., Meyts, Isabelle

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Author Correction: GIMAP5 deficiency reveals a mammalian ceramide-driven longevity assurance pathway von Park, Ann Y., Leney-Greene, Michael, Lynberg, Matthew, Gabrielski, Justin Q., Xu, Xijin, Schwarz, Benjamin, Zheng, Lixin, Balasubramaniyam, Arasu, Ham, Hyoungjun, Chao, Brittany, Zhang, Yu, Matthews, Helen F., Cui, Jing, Yao, Yikun, Kubo, Satoshi, Chanchu, Jean Michel, Morawski, Aaron R., Cook, Sarah A., Jiang, Ping, Ravell, Juan C., Cheng, Yan H., George, Alex, Faruqi, Aiman, Pagalilauan, Alison M., Bergerson, Jenna R. E., Ganesan, Sundar, Chauvin, Samuel D., Aluri, Jahnavi, Edwards-Hicks, Joy, Bohrnsen, Eric, Tippett, Caroline, Omar, Habib, Xu, Leilei, Butcher, Geoffrey W., Pascall, John, Karakoc-Aydiner, Elif, Kiykim, Ayca, Maecker, Holden, Tezcan, İlhan, Esenboga, Saliha, Heredia, Raul Jimenez, Akata, Deniz, Tekin, Saban, Kara, Altan, Kuloglu, Zarife, Unal, Emel, Kendirli, Tanıl, Dogu, Figen, Karabiber, Esra, Atkinson, T. Prescott, Cochet, Claude, Filhol, Odile, Bosio, Catherine M., Davis, Mark M., Lifton, Richard P., Pearce, Erika L., Daumke, Oliver, Aytekin, Caner, Şahin, Gülseren Evirgen, Aksu, Aysel Ünlüsoy, Uzel, Gulbu, Koneti Rao, V., Sari, Sinan, Dalgıç, Buket, Boztug, Kaan, Cagdas, Deniz, Haskologlu, Sule, Ikinciogullari, Aydan, Schwefel, David, Vilarinho, Silvia, Baris, Safa, Ozen, Ahmet, Su, Helen C., Lenardo, Michael J.

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SARS-CoV-2 Spike Protein-Directed Monoclonal Antibodies May Ameliorate COVID-19 Complications in APECED Patients von Ferre, Elise M. N., Schmitt, Monica M., Ochoa, Sebastian, Rosen, Lindsey B., Shaw, Elana R., Burbelo, Peter D., Stoddard, Jennifer L., Rampertaap, Shakuntala, DiMaggio, Tom, Bergerson, Jenna R. E., Rosenzweig, Sergio D., Notarangelo, Luigi D., Holland, Steven M., Lionakis, Michail S.

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Treatment of STAT3-deficient hyper–immunoglobulin E syndrome with monoclonal antibodies targeting allergic inflammation von James, Alyssa E., West, Laura, Schloss, Katheryn, Nataraj, Pavan, Urban, Amanda, Hirsch, Aleksandra, Krausz, Máté, Kumar, Shashi, Raasch, Jason, Risma, Kimberly, Church, Joseph A., Grimbacher, Bodo, Bergerson, Jenna R.E., Chong, Hey, Freeman, Alexandra F.

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Evaluation and Management of Deficiency of Adenosine Deaminase 2: An International Consensus Statement von Lee, Pui Y, Davidson, Brad A, Abraham, Roshini S, Alter, Blanche, Arostegui, Juan I, Bell, Katherine, Belot, Alexandre, Bergerson, Jenna R E, Bernard, Timothy J, Brogan, Paul A, Berkun, Yackov, Deuitch, Natalie T, Dimitrova, Dimana, Georgin-Lavialle, Sophie A, Gattorno, Marco, Grimbacher, Bodo, Hashem, Hasan, Hershfield, Michael S, Ichord, Rebecca N, Izawa, Kazushi, Kanakry, Jennifer A, Khubchandani, Raju P, Klouwer, Femke C C, Luton, Evan A, Man, Ada W, Meyts, Isabelle, Van Montfrans, Joris M, Ozen, Seza, Saarela, Janna, Santo, Gustavo C, Sharma, Aman, Soldatos, Ariane, Sparks, Rachel, Torgerson, Troy R, Uriarte, Ignacio Leandro, Youngstein, Taryn A B, Zhou, Qing, Aksentijevich, Ivona, Kastner, Daniel L, Chambers, Eugene P, Ombrello, Amanda K

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CD4 T cell–restricted IL-2 signaling defect in a patient with a novel IFNGR1 deficiency von Khanolkar, Aaruni, Kirschmann, Dawn A., Caparelli, Edward A., Wilks, Jeffrey D., Cerullo, Jillian M., Bergerson, Jenna R.E., Jennings, Lawrence J., Fuleihan, Ramsay L.

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Vulnerability of pediatric patients with mitochondrial disease to vaccine-preventable diseases von Kruk, Shannon K., Pacheco, Susan E., Koenig, Mary Kay, Bergerson, Jenna R.E., Gordon-Lipkin, Eliza, McGuire, Peter J.

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A multifaceted disease: The stats of STAT3 GOF von Freeman, Alexandra F., Bergerson, Jenna R.E.

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Antibody responses to the SARS-CoV-2 vaccine in individuals with various inborn errors of immunity von Delmonte, Ottavia M., Bergerson, Jenna R.E., Burbelo, Peter D., Durkee-Shock, Jessica R., Dobbs, Kerry, Bosticardo, Marita, Keller, Michael D., McDermott, David H., Rao, V. Koneti, Dimitrova, Dimana, Quiros-Roldan, Eugenia, Imberti, Luisa, Ferrè, Elise M.N., Schmitt, Monica, Lafeer, Christine, Pfister, Justina, Shaw, Dawn, Draper, Deborah, Truong, Meng, Ulrick, Jean, DiMaggio, Tom, Urban, Amanda, Holland, Steven M., Lionakis, Michail S., Cohen, Jeffrey I., Ricotta, Emily E., Notarangelo, Luigi D., Freeman, Alexandra F.

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SASH3 variants cause a novel form of X-linked combined immunodeficiency with immune dysregulation von Delmonte, Ottavia M., Bergerson, Jenna R.E., Kawai, Tomoki, Kuehn, Hye Sun, McDermott, David H., Cortese, Irene, Zimmermann, Michael T., Dobbs, A. Kerry, Bosticardo, Marita, Fink, Danielle, Majumdar, Shamik, Palterer, Boaz, Pala, Francesca, Dsouza, Nikita R., Pouzolles, Marie, Taylor, Naomi, Calvo, Katherine R., Daley, Stephen R., Velez, Daniel, Agharahimi, Anahita, Myint-Hpu, Katherine, Dropulic, Lesia K., Lyons, Jonathan J., Holland, Steven M., Freeman, Alexandra F., Ghosh, Rajarshi, Similuk, Morgan B., Niemela, Julie E., Stoddard, Jennifer, Kuhns, Douglas B., Urrutia, Raul, Rosenzweig, Sergio D., Walkiewicz, Magdalena A., Murphy, Philip M., Notarangelo, Luigi D.

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Tip of the iceberg: A comprehensive review of liver disease in Inborn errors of immunity von Sharma, Disha, Ben Yakov, Gil, Kapuria, Devika, Viana Rodriguez, Gracia, Gewirtz, Meital, Haddad, James, Kleiner, David E., Koh, Christopher, Bergerson, Jenna R. E., Freeman, Alexandra F., Heller, Theo

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GIMAP5 deficiency reveals a mammalian ceramide-driven longevity assurance pathway von Park, Ann Y., Leney-Greene, Michael, Lynberg, Matthew, Gabrielski, Justin Q., Xu, Xijin, Schwarz, Benjamin, Zheng, Lixin, Balasubramaniyam, Arasu, Ham, Hyoungjun, Chao, Brittany, Zhang, Yu, Matthews, Helen F., Cui, Jing, Yao, Yikun, Kubo, Satoshi, Chanchu, Jean Michel, Morawski, Aaron R., Cook, Sarah A., Jiang, Ping, Ravell, Juan C., Cheng, Yan H., George, Alex, Faruqi, Aiman, Pagalilauan, Alison M., Bergerson, Jenna R. E., Ganesan, Sundar, Chauvin, Samuel D., Aluri, Jahnavi, Edwards-Hicks, Joy, Bohrnsen, Eric, Tippett, Caroline, Omar, Habib, Xu, Leilei, Butcher, Geoffrey W., Pascall, John, Karakoc-Aydiner, Elif, Kiykim, Ayca, Maecker, Holden, Tezcan, İlhan, Esenboga, Saliha, Heredia, Raul Jimenez, Akata, Deniz, Tekin, Saban, Kara, Altan, Kuloglu, Zarife, Unal, Emel, Kendirli, Tanıl, Dogu, Figen, Karabiber, Esra, Atkinson, T. Prescott, Cochet, Claude, Filhol, Odile, Bosio, Catherine M., Davis, Mark M., Lifton, Richard P., Pearce, Erika L., Daumke, Oliver, Aytekin, Caner, Şahin, Gülseren Evirgen, Aksu, Aysel Ünlüsoy, Uzel, Gulbu, Koneti Rao, V., Sari, Sinan, Dalgıç, Buket, Boztug, Kaan, Cagdas, Deniz, Haskologlu, Sule, Ikinciogullari, Aydan, Schwefel, David, Vilarinho, Silvia, Baris, Safa, Ozen, Ahmet, Su, Helen C., Lenardo, Michael J.

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Prospective evaluation of patients with non‐cirrhotic portal hypertension: A single centre study von Mironova, Maria, Gopalakrishna, Harish, Viana Rodriguez, Gracia Maria, Abdul Majeed, Nehna, Hitawala, Asif A., Fuss, Ivan J., Bergerson, Jenna R. E., Faust, Alison J., Laurin, Jacqueline M., Norman‐Wheeler, Jaha, Scott, Shani, Hercun, Julian, Redd, Bernadette, Kleiner, David E., Koh, Christopher, Heller, Theo

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Clinical exome sequencing of 1000 families with complex immune phenotypes: Toward comprehensive genomic evaluations von Similuk, Morgan N, Yan, Jia, Ghosh, Rajarshi, Oler, Andrew J, Franco, Luis M, Setzer, Michael R, Kamen, Michael, Jodarski, Colleen, DiMaggio, Thomas, Davis, Joie, Gore, Rachel, Jamal, Leila, Borges, Adrienne, Gentile, Nicole, Niemela, Julie, Lowe, Chenery, Jevtich, Kathleen, Yu, Yunting, Hullfish, Haley, Hsu, Amy P, Hong, Celine, Littel, Patricia, Seifert, Bryce A, Milner, Joshua, Johnston, Jennifer J, Cheng, Xi, Li, Zhiwen, Veltri, Daniel, Huang, Ke, Kaladi, Krishnaveni, Barnett, Jason, Zhang, Lingwen, Vlasenko, Nikita, Fan, Yongjie, Karlins, Eric, Ganakammal, Satishkumar Ranganathan, Gilmore, Robert, Tran, Emily, Yun, Alvin, Mackey, Joseph, Yazhuk, Svetlana, Lack, Justin, Kuram, Vasudev, Cao, Wenjia, Huse, Susan, Frank, Karen, Fahle, Gary, Rosenzweig, Sergio, Su, Yan, Hwang, SuJin, Bi, Weimin, Bennett, John, Myles, Ian A, De Ravin, Suk See, Fuss, Ivan, Strober, Warren, Bielekova, Bibiana, Almeida de Jesus, Adriana, Goldbach-Mansky, Raphaela, Williamson, Peter, Kumar, Kelly, Dempsy, Caeden, Frischmeyer-Guerrerio, Pamela, Fisch, Robin, Bolan, Hyejeong, Metcalfe, Dean D, Komarow, Hirsh, Carter, Melody, Druey, Kirk M, Sereti, Irini, Dropulic, Lesia, Klion, Amy D, Khoury, Paneez, O' Connell, Elise M, Holland-Thomas, Nicole C, Brown, Thomas, McDermott, David H, Murphy, Philip M, Bundy, Vanessa, Keller, Michael D, Peng, Christine, Kim, Helen, Norman, Stephanie, Delmonte, Ottavia M, Kang, Elizabeth, Su, Helen C, Malech, Harry, Freeman, Alexandra, Zerbe, Christa, Uzel, Gulbu, Bergerson, Jenna R E, Rao, V Koneti, Olivier, Kenneth N, Lyons, Jonathan J, Lisco, Andrea, Cohen, Jeffrey I, Lionakis, Michail S, Biesecker, Leslie G, Xirasagar, Sandhya, Notarangelo, Luigi D

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Nodular regenerative hyperplasia in X-linked agammaglobulinemia: An underestimated and severe complication von Nunes-Santos, Cristiane J., Koh, Christopher, Rai, Anjali, Sacco, Keith, Marciano, Beatriz E., Kleiner, David E., Marko, Jamie, Bergerson, Jenna R.E., Stack, Michael, Rivera, Maria M., Constantine, Gregory, Strober, Warren, Uzel, Gulbu, Fuss, Ivan J., Notarangelo, Luigi D., Holland, Steven M., Rosenzweig, Sergio D., Heller, Theo

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Development of hepatic fibrosis in common variable immunodeficiency‐related porto‐sinusoidal vascular disorder von Hercun, Julian, Asif, Bilal, Vittal, Anusha, Ahmed, Abdel, Gopalakrishna Pillai, Harish Kumar, Bergerson, Jenna R. E., Holland, Steven, Uzel, Gulbu, Strober, Warren, Fuss, Ivan J., Koh, Christopher, Kleiner, David E., Heller, Theo

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Perturbations of the T-cell receptor repertoire in response to SARS-CoV-2 in immunocompetent and immunocompromised individuals von Delmonte, Ottavia M., Oguz, Cihan, Dobbs, Kerry, Myint-Hpu, Katherine, Palterer, Boaz, Abers, Michael S., Draper, Deborah, Truong, Meng, Kaplan, Ian M., Gittelman, Rachel M., Zhang, Yu, Rosen, Lindsey B., Snow, Andrew L., Dalgard, Clifton L., Burbelo, Peter D., Imberti, Luisa, Sottini, Alessandra, Quiros-Roldan, Eugenia, Castelli, Francesco, Rossi, Camillo, Brugnoni, Duilio, Biondi, Andrea, Bettini, Laura Rachele, D’Angio, Mariella, Bonfanti, Paolo, Anderson, Megan V., Saracino, Annalisa, Chironna, Maria, Di Stefano, Mariantonietta, Fiore, Jose Ramon, Santantonio, Teresa, Castagnoli, Riccardo, Marseglia, Gian Luigi, Magliocco, Mary, Bosticardo, Marita, Pala, Francesca, Shaw, Elana, Matthews, Helen, Weber, Sarah E., Xirasagar, Sandhya, Barnett, Jason, Oler, Andrew J., Dimitrova, Dimana, Bergerson, Jenna R.E., McDermott, David H., Rao, V. Koneti, Murphy, Philip M., Holland, Steven M., Lisco, Andrea, Su, Helen C., Lionakis, Michail S., Cohen, Jeffrey I., Freeman, Alexandra F., Snyder, Thomas M., Lack, Justin, Notarangelo, Luigi D.

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Artificial thymic organoids represent a reliable tool to study T-cell differentiation in patients with severe T-cell lymphopenia von Bosticardo, Marita, Pala, Francesca, Calzoni, Enrica, Delmonte, Ottavia M., Dobbs, Kerry, Gardner, Cameron L., Sacchetti, Nicolo', Kawai, Tomoki, Garabedian, Elizabeth K., Draper, Debbie, Bergerson, Jenna R.E., DeRavin, Suk See, Freeman, Alexandra F., Güngör, Tayfun, Hartog, Nicholas, Holland, Steven M., Kohn, Donald B., Malech, Harry L., Markert, Mary Louise, Weinacht, Katja G., Villa, Anna, Seet, Christopher S., Montel-Hagen, Amelie, Crooks, Gay M., Notarangelo, Luigi D.

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Characterization of the antispike IgG immune response to COVID-19 vaccines in people with a wide variety of immunodeficiencies von Zendt, Mackenzie, Bustos Carrillo, Fausto A, Kelly, Sophie, Saturday, Taylor, DeGrange, Maureen, Ginigeme, Anita, Wu, Lurline, Callier, Viviane, Ortega-Villa, Ana, Faust, Mondreakest, Chang-Rabley, Emma, Bugal, Kara, Kenney, Heather, Khil, Pavel, Youn, Jung-Ho, Osei, Gloria, Regmi, Pravesh, Anderson, Victoria, Bosticardo, Marita, Daub, Janine, DiMaggio, Thomas, Kreuzburg, Samantha, Pala, Francesca, Pfister, Justina, Treat, Jennifer, Ulrick, Jean, Karkanitsa, Maria, Kalish, Heather, Kuhns, Douglas B, Priel, Debra L, Fink, Danielle L, Tsang, John S, Sparks, Rachel, Uzel, Gulbu, Waldman, Meryl A, Zerbe, Christa S, Delmonte, Ottavia M, Bergerson, Jenna R E, Das, Sanchita, Freeman, Alexandra F, Lionakis, Michail S, Sadtler, Kaitlyn, van Doremalen, Neeltje, Munster, Vincent, Notarangelo, Luigi D, Holland, Steven M, Ricotta, Emily E

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