Perturbed Redox Signaling Exacerbates a Mitochondrial Myopathy von Dogan, Sukru Anil, Cerutti, Raffaele, Benincá, Cristiane, Brea-Calvo, Gloria, Jacobs, Howard Trevor, Zeviani, Massimo, Szibor, Marten, Viscomi, Carlo

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Opa1 Overexpression Protects from Early-Onset Mpv17−/−-Related Mouse Kidney Disease von Luna-Sanchez, Marta, Benincá, Cristiane, Cerutti, Raffaele, Brea-Calvo, Gloria, Yeates, Anna, Scorrano, Luca, Zeviani, Massimo, Viscomi, Carlo

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Utilization of Human Samples for Assessment of Mitochondrial Bioenergetics: Gold Standards, Limitations, and Future Perspectives von Acin-Perez, Rebeca, Benincá, Cristiane, Shabane, Byourak, Shirihai, Orian S, Stiles, Linsey

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The BCKDK inhibitor BT2 is a chemical uncoupler that lowers mitochondrial ROS production and de novo lipogenesis von Acevedo, Aracely, Jones, Anthony E., Danna, Bezawit T., Turner, Rory, Montales, Katrina P., Benincá, Cristiane, Reue, Karen, Shirihai, Orian S., Stiles, Linsey, Wallace, Martina, Wang, Yibin, Bertholet, Ambre M., Divakaruni, Ajit S.

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Selective Disruption of Mitochondrial Thiol Redox State in Cells and In Vivo von Booty, Lee M., Gawel, Justyna M., Cvetko, Filip, Caldwell, Stuart T., Hall, Andrew R., Mulvey, John F., James, Andrew M., Hinchy, Elizabeth C., Prime, Tracy A., Arndt, Sabine, Beninca, Cristiane, Bright, Thomas P., Clatworthy, Menna R., Ferdinand, John R., Prag, Hiran A., Logan, Angela, Prudent, Julien, Krieg, Thomas, Hartley, Richard C., Murphy, Michael P.

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Gαq signalling: The new and the old von Sánchez-Fernández, Guzmán, Cabezudo, Sofía, García-Hoz, Carlota, Benincá, Cristiane, Aragay, Anna M., Mayor, Federico, Ribas, Catalina

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Basal mitophagy is widespread in Drosophila but minimally affected by loss of Pink1 or parkin von Lee, Juliette J, Sanchez-Martinez, Alvaro, Martinez Zarate, Aitor, Benincá, Cristiane, Mayor, Ugo, Clague, Michael J, Whitworth, Alexander J

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Tetra-arylborate lipophilic anions as targeting groups von Gaddale Devanna, Kishore K, Gawel, Justyna M, Prime, Tracy A, Cvetko, Filip, Benincá, Cristiane, Caldwell, Stuart T, Negoda, Alexander, Harrison, Andrew, James, Andrew M, Pavlov, Evgeny V, Murphy, Michael P, Hartley, Richard C

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Rapamycin rescues mitochondrial myopathy via coordinated activation of autophagy and lysosomal biogenesis von Civiletto, Gabriele, Dogan, Sukru Anil, Cerutti, Raffaele, Fagiolari, Gigliola, Moggio, Maurizio, Lamperti, Costanza, Benincá, Cristiane, Viscomi, Carlo, Zeviani, Massimo

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A new non-canonical pathway of Gα(q) protein regulating mitochondrial dynamics and bioenergetics von Benincá, Cristiane, Planagumà, Jesús, de Freitas Shuck, Adriana, Acín-Perez, Rebeca, Muñoz, Juan Pablo, de Almeida, Marina Mateus, Brown, Joan H, Murphy, Anne N, Zorzano, Antonio, Enríquez, Jose Antonio, Aragay, Anna M

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Inhibition of proteasome rescues a pathogenic variant of respiratory chain assembly factor COA7 von Mohanraj, Karthik, Wasilewski, Michal, Benincá, Cristiane, Cysewski, Dominik, Poznanski, Jaroslaw, Sakowska, Paulina, Bugajska, Zaneta, Deckers, Markus, Dennerlein, Sven, Fernandez‐Vizarra, Erika, Rehling, Peter, Dadlez, Michal, Zeviani, Massimo, Chacinska, Agnieszka

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Inhibition of ATP synthase reverse activity restores energy homeostasis in mitochondrial pathologies von Acin‐Perez, Rebeca, Benincá, Cristiane, Fernandez del Rio, Lucia, Shu, Cynthia, Baghdasarian, Siyouneh, Zanette, Vanessa, Gerle, Christoph, Jiko, Chimari, Khairallah, Ramzi, Khan, Shaharyar, Rincon Fernandez Pacheco, David, Shabane, Byourak, Erion, Karel, Masand, Ruchi, Dugar, Sundeep, Ghenoiu, Cristina, Schreiner, George, Stiles, Linsey, Liesa, Marc, Shirihai, Orian S

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Neurodevelopmental regression, severe generalized dystonia, and metabolic acidosis caused by POLR3A mutations von Zanette, Vanessa, Reyes, Aurelio, Johnson, Mark, do Valle, Daniel, Robinson, Alan J., Monteiro, Vaneisse, Telles, Bruno Augusto, L.R. Souza, Ricardo, S.F. Santos, Mara L, Benincá, Cristiane, Zeviani, Massimo

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Chronic genetic damages in Geophagus brasiliensis exposed to anthropic impact in Estuarine Lakes at Santa Catarina Coast–Southern of Brazil von Benincá, Cristiane, Ramsdorf, Wanessa, Vicari, Taynah, de Oliveira Ribeiro, Ciro A., de Almeida, Marina I., Silva de Assis, Helena C., Cestari, Marta Margarete

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Pro-inflammatory macrophage activation does not require inhibition of oxidative phosphorylation von Ball, Andréa B, Jones, Anthony E, Nguyễn, Kaitlyn B, Rios, Amy, Marx, Nico, Hsieh, Wei Yuan, Yang, Krista, Desousa, Brandon R, Kim, Kristen K O, Veliova, Michaela, Del Mundo, Zena Marie, Shirihai, Orian S, Benincá, Cristiane, Stiles, Linsey, Bensinger, Steven J, Divakaruni, Ajit S

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A novel approach to measure complex V ATP hydrolysis in frozen cell lysates and tissue homogenates von Fernandez-Del-Rio, Lucia, Benincá, Cristiane, Villalobos, Frankie, Shu, Cynthia, Stiles, Linsey, Liesa, Marc, Divakaruni, Ajit S, Acin-Perez, Rebeca, Shirihai, Orian S

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A mammalian-specific Alex3/Gα q protein complex regulates mitochondrial trafficking, dendritic complexity, and neuronal survival von Izquierdo-Villalba, Ismael, Mirra, Serena, Manso, Yasmina, Parcerisas, Antoni, Rubio, Javier, Del Valle, Jaume, Gil-Bea, Francisco J, Ulloa, Fausto, Herrero-Lorenzo, Marina, Verdaguer, Ester, Benincá, Cristiane, Castro-Torres, Rubén D, Rebollo, Elena, Marfany, Gemma, Auladell, Carme, Navarro, Xavier, Enríquez, José A, López de Munain, Adolfo, Soriano, Eduardo, Aragay, Anna M

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APOPT1/COA8 assists COX assembly and is oppositely regulated by UPS and ROS von Signes, Alba, Cerutti, Raffaele, Dickson, Anna S, Benincá, Cristiane, Hinchy, Elizabeth C, Ghezzi, Daniele, Carrozzo, Rosalba, Bertini, Enrico, Murphy, Michael P, Nathan, James A, Viscomi, Carlo, Fernandez‐Vizarra, Erika, Zeviani, Massimo

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NDUFV1 mutations in complex I deficiency: Case reports and review of symptoms von Zanette, Vanessa, Valle, Daniel do, Telles, Bruno Augusto, Robinson, Alan J., Monteiro, Vaneisse, Santos, Mara Lucia S. F., Souza, Ricardo Lehtonen R., Benincá, Cristiane

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Mitochondrial diseases: from mechanisms to therapies von Viscomi, Carlo, Dogan, Anil, Cerutti, Raffaele, Civiletto, Gabriele, Beninca’, Cristiane, Fagiolari, Gigliola, Moggio, Maurizio, Jacobs, Howy, Szibor, Marten, Zeviani, Massimo

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