Bone marrow–derived mesenchymal stem cells remain host-derived despite successful hematopoietic engraftment after allogeneic transplantation in patients with lysosomal and peroxiso... von Koç, Omer N., Peters, Charles, Aubourg, Patrick, Raghavan, Shrini, Dyhouse, Stephanie, DeGasperi, Rita, Kolodny, Edwin H., BenYoseph, Yoav, Gerson, Stanton L., Lazarus, Hillard M., Caplan, Arnold I., Watkins, Paul A., Krivit, William

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Rapid detection of common metachromatic leukodystrophy mutations by restriction analysis of arylsulfatase A gene amplimers von Ben-Yoseph, Yoav, Mitchell, Deborah A.

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Discrimination Between Metachromatic Leukodystrophy and Pseudo-Deficiency of Arylsulfatase A by Restriction Digest of Amplified Gene Fragments von Ben-Yoseph, Yoav, Mitchell, Deborah A.

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Detection of kinetically abnormal argininosuccinate synthase in neonatal citrullinemia by conversion of citrulline to arginine in intact fibroblasts von Ben-Yoseph, Yoav, Mitchell, Deborah A.

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Substrate-specificities of acid and alkaline ceramidases in fibroblasts from patients with Farber disease and controls von Momoi, T, Ben-Yoseph, Y, Nadler, H L

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Radiometric assays of N-acetylglucosaminylphosphotransferase and α- N-acetylglucosaminyl phosphodiesterase with substrates labeled in the glucosamine moiety von Ben-Yoseph, Yoav, Baylerian, Michael S., Nadler, Henry L.

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Prenatal Diagnosis of I-cell Disease in the First and Second Trimesters von Parvathy, M.R., Mitchell, Deborah A., Ben-Yoseph, Yoav

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Lysosomal enzyme activities in fresh and frozen chorionic villi and in cultured trophoblasts von Ben-Yoseph, Yoav, Evans, Mark I., Bottoms, Sydney F., Pack, Beverley A., Mitchell, Deborah A., Koppitch, Fredrick C., Nadler, Henry L.

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Galactosylceramide β-galactosidase in krabbe disease: Partial purification and characterization of the mutant enzyme von Ben-Yoseph, Yoav, Hungerford, Melinda, Nadler, Henry L.

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Purification and properties of neutral β-galactosidases from human liver von Ben-Yoseph, Yoav, Shapira, Emmanuel, Edelman, David, Burton, Barbara K., Nadler, Henry L.

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Mannosylation of glycoproteins and dolichol derivatives in fibroblasts from patients with cystic fibrosis von Ben-Yoseph, Yoav, DeFranco, C.L., Nadler, Henry L.

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Km defect in neuraminidase of dysmorphic type sialidosis with and without β-galactosidase deficiency von Ben-Yoseph, Yoav, Momoi, Toru, Baylerian, Michael S., Nadler, Henry L.

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Antibody-mediated thermal stabilization of human hexosaminidases von Ben-Yoseph, Yoav, Geiger, Benjamin, Arnon, Ruth

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Immunological relationships among hexosaminidases of different species von Geiger, Benjamin, Ben-Yoseph, Yoav, Arnon, Ruth

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Multiple carbohydrate-cleaving specificities in human acidic and neutral glycosidases von Ben-Yoseph, Yoav, Fiddler, Morris B., Rousson, Robert, Nadler, Henry L.

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Maternal serum hexosaminidase A in pregnancy: Effects of gestational age and fetal genotype von Ben-Yoseph, Yoav, Pack, Beverley A., Thomas, Pamela M., Nadler, Henry L., Kaback, Michael M., Optiz, John M., Reynolds, James F.

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