Astrocyte Glutamine Synthetase: Importance in Hyperammonemic Syndromes and Potential Target for Therapy von Brusilow, Saul W., Koehler, Raymond C., Traystman, Richard J., Cooper, Arthur J.L.

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Survival after Treatment with Phenylacetate and Benzoate for Urea-Cycle Disorders von Enns, Gregory M, Berry, Susan A, Berry, Gerard T, Rhead, William J, Brusilow, Saul W, Hamosh, Ada

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Hyperammonemic encephalopathy von Brusilow, Saul W

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Neonatal onset ornithine transcarbamylase deficiency: A retrospective analysis von Maestri, Nancy E., Clissold, David, Brusilow, Saul W.

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Encephalopathy in acute liver failure resulting from acetaminophen intoxication: New observations with potential therapy von Brusilow, Saul W, Cooper, Arthur J. L

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Long-Term Treatment of Girls with Ornithine Transcarbamylase Deficiency von Maestri, Nancy E, Brusilow, Saul W, Clissold, David B, Bassett, Susan S

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Preserved hypocapnic pial arteriolar constriction during hyperammonemia by glutamine synthetase inhibition von Hirata, Takahiko, Kawaguchi, Tetsu, Brusilow, Saul W, Traystman, Richard J, Koehler, Raymond C

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Urea cycle disorders : Diagnosis, pathophysiology, and therapy von BRUSILOW, S. W, MAESTRI, N. E

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Glutamine-dependent inhibition of pial arteriolar dilation to acetylcholine with and without hyperammonemia in the rat von Kawaguchi, Tetsu, Brusilow, Saul W, Traystman, Richard J, Koehler, Raymond C

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Phenylacetylglutamine may replace urea as a vehicle for waste nitrogen excretion von BRUSILOW, S. W

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The phenotype of ostensibly healthy women who are carriers for ornithine transcarbamylase deficiency von Maestri, N E, Lord, C, Glynn, M, Bale, A, Brusilow, S W

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Induction of fetal hemoglobin synthesis in children with sickle cell anemia on low-dose oral sodium phenylbutyrate therapy von RESAR, Linda M. S, SEGAL, Jodi B, FITZPATRIC, Lorna K, FRIEDMANN, Alison, BRUSILOW, Saul W, DOVER, George J

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Hyperammonemia in Women with a Mutation at the Ornithine Carbamoyltransferase Locus: A Cause of Postpartum Coma von Arn, Pamela Hawks, Hauser, Elizabeth R, Thomas, George H, Herman, Gail, Hess, David, Brusilow, Saul W

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Prospective treatment of urea cycle disorders von Maestri, Nancy E., Hauser, Elizabeth R., Bartholomew, Dennis, Brusilow, Saul W.

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Waste nitrogen excretion via amino acid acylation: benzoate and phenylacetate in lysinuric protein intolerance von SIMELL, O, SIPILA, I, RAJANTIE, J, VALLE, D. L, BRUSILOW, S. W

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Hypocapnia von Carey, Brian J

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Interaction of glutamine and arginine on cerebrovascular reactivity to hypercapnia von Okada, Toshiki, Watanabe, Yukinaga, Brusilow, Saul W, Traystman, Richard J, Koehler, Raymond C

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Allopurinol-Induced Orotidinuria: A Test for Mutations at the Ornithine Carbamoyltransferase Locus in Women von Hauser, Elizabeth R, Finkelstein, Janice E, Valle, David, Brusilow, Saul W

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Impaired pial arteriolar reactivity to hypercapnia during hyperammonemia depends on glutamine synthesis von Hirata, T, Koehler, R C, Kawaguchi, T, Brusilow, S W, Traystman, R J

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Oral Sodium Phenylbutyrate Therapy in Homozygous β Thalassemia: A Clinical Trial von Collins, Anne F., Pearson, Howard A., Giardina, Patricia, McDonagh, Kevin T., Brusilow, Saul W., Dover, George J.

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