mRNA Translation Gone Awry: Translation Fidelity and Neurological Disease von Kapur, Mridu, Ackerman, Susan L.

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Regulation of mRNA Translation in Neurons—A Matter of Life and Death von Kapur, Mridu, Monaghan, Caitlin E., Ackerman, Susan L.

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Ribosome stalling induced by mutation of a CNS-specific tRNA causes neurodegeneration von Ishimura, Ryuta, Nagy, Gabor, Dotu, Ivan, Zhou, Huihao, Yang, Xiang-Lei, Schimmel, Paul, Senju, Satoru, Nishimura, Yasuharu, Chuang, Jeffrey H., Ackerman, Susan L.

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Mutation of a U2 snRNA Gene Causes Global Disruption of Alternative Splicing and Neurodegeneration von Jia, Yichang, Mu, John C., Ackerman, Susan L.

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Regulation of ex-translational activities is the primary function of the multi-tRNA synthetase complex von Cui, Haissi, Kapur, Mridu, Diedrich, Jolene K, Yates, John R, Ackerman, Susan L, Schimmel, Paul

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Endothelial Unc5B controls blood-brain barrier integrity von Boyé, Kevin, Geraldo, Luiz Henrique, Furtado, Jessica, Pibouin-Fragner, Laurence, Poulet, Mathilde, Kim, Doyeun, Nelson, Bryce, Xu, Yunling, Jacob, Laurent, Maissa, Nawal, Agalliu, Dritan, Claesson-Welsh, Lena, Ackerman, Susan L., Eichmann, Anne

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Activation of GCN2 kinase by ribosome stalling links translation elongation with translation initiation von Ishimura, Ryuta, Nagy, Gabor, Dotu, Ivan, Chuang, Jeffrey H, Ackerman, Susan L

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Mutations in the microtubule-associated protein 1A (Map1a) gene cause Purkinje cell degeneration von Liu, Ye, Lee, Jeong Woong, Ackerman, Susan L

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Seryl-tRNA synthetase promotes translational readthrough by mRNA binding and involvement of the selenocysteine incorporation machinery von Liu, Ze, Wang, Justin, Shi, Yi, Yee, Brian A, Terrey, Markus, Zhang, Qian, Lee, Jenq-Chang, Lin, Kuo-I, Wang, Andrew H-J, Ackerman, Susan L, Yeo, Gene W, Cui, Haissi, Yang, Xiang-Lei

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A deficiency of ceramide biosynthesis causes cerebellar purkinje cell neurodegeneration and lipofuscin accumulation von Zhao, Lihong, Spassieva, Stefka D, Jucius, Thomas J, Shultz, Leonard D, Shick, H Elizabeth, Macklin, Wendy B, Hannun, Yusuf A, Obeid, Lina M, Ackerman, Susan L

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Notch signaling regulates UNC5B to suppress endothelial proliferation, migration, junction activity, and retinal plexus branching von Raza, Qanber, Nadeem, Taliha, Youn, Seock-Won, Swaminathan, Bhairavi, Gupta, Ahana, Sargis, Timothy, Du, Jing, Cuervo, Henar, Eichmann, Anne, Ackerman, Susan L., Naiche, L. A., Kitajewski, Jan

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Defects in translation-dependent quality control pathways lead to convergent molecular and neurodevelopmental pathology von Terrey, Markus, Adamson, Scott, Chuang, Jeffrey H., Ackerman, Susan L.

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Deficiencies in tRNA synthetase editing activity cause cardioproteinopathy von Liu, Ye, Satz, Jakob S., Vo, My-Nuong, Nangle, Leslie A., Schimmel, Paul, Ackerman, Susan L.

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Editing-defective tRNA synthetase causes protein misfolding and neurodegeneration von Longo-Guess, Chantal M, Sundberg, John P, Davisson, Muriel T, Schimmel, Paul, Ackerman, Susan L, Lee, Jeong Woong, Beebe, Kirk, Jang, Jaeseon, Nangle, Leslie A, Cook, Susan A

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GTPBP1 resolves paused ribosomes to maintain neuronal homeostasis von Terrey, Markus, Adamson, Scott, Gibson, Alana L., Deng, Tianda, Ishimura, Ryuta, Chuang, Jeffrey H., Ackerman, Susan L.

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The UNC5C netrin receptor regulates dorsal guidance of mouse hindbrain axons von Kim, Doyeun, Ackerman, Susan L

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Alteration of the unfolded protein response modifies neurodegeneration in a mouse model of Marinesco–Sjögren syndrome von Zhao, Lihong, Rosales, Christine, Seburn, Kevin, Ron, David, Ackerman, Susan L.

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Unc5C and DCC act downstream of Ctip2 and Satb2 and contribute to corpus callosum formation von Srivatsa, Swathi, Parthasarathy, Srinivas, Britanova, Olga, Bormuth, Ingo, Donahoo, Amber-Lee, Ackerman, Susan L., Richards, Linda J., Tarabykin, Victor

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Synergistic integration of Netrin and ephrin axon guidance signals by spinal motor neurons von Poliak, Sebastian, Morales, Daniel, Croteau, Louis-Philippe, Krawchuk, Dayana, Palmesino, Elena, Morton, Susan, Cloutier, Jean-François, Charron, Frederic, Dalva, Matthew B, Ackerman, Susan L, Kao, Tzu-Jen, Kania, Artur

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Endoplasmic reticulum stress in health and disease von Zhao, Lihong, Ackerman, Susan L

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