The Logic of the 26S Proteasome von Collins, Galen Andrew, Goldberg, Alfred L.

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Proteasome-Mediated Processing of Nrf1 Is Essential for Coordinate Induction of All Proteasome Subunits and p97 von Sha, Zhe, Goldberg, Alfred L.

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Muscle wasting in disease: molecular mechanisms and promising therapies von Cohen, Shenhav, Nathan, James A., Goldberg, Alfred L.

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Impact of Genetics on the Clinical Management of Channelopathies von Schwartz, Peter J., MD, Ackerman, Michael J., MD, PhD, George, Alfred L., MD, Wilde, Arthur A.M., MD, PhD

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Evolution: Untangling the woolly mammoth von Roca, Alfred L.

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The deubiquitinating enzyme Usp14 allosterically inhibits multiple proteasomal activities and ubiquitin-independent proteolysis von Kim, Hyoung Tae, Goldberg, Alfred L.

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UBL domain of Usp14 and other proteins stimulates proteasome activities and protein degradation in cells von Kim, Hyoung Tae, Goldberg, Alfred L.

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In Memoriam Arthur J. Atkinson, Jr. (1938–2024) von Lertora, Juan J. L., Huang, Shiew‐Mei, George, Alfred L.

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Strain- and age-dependent hippocampal neuron sodium currents correlate with epilepsy severity in Dravet syndrome mice von Mistry, Akshitkumar M, Thompson, Christopher H, Miller, Alison R, Vanoye, Carlos G, George,, Alfred L, Kearney, Jennifer A

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De novo KCNB1 mutations in epileptic encephalopathy von Torkamani, Ali, Bersell, Kevin, Jorge, Benjamin S., Bjork Jr, Robert L., Friedman, Jennifer R., Bloss, Cinnamon S., Cohen, Julie, Gupta, Siddharth, Naidu, Sakkubai, Vanoye, Carlos G., George Jr, Alfred L., Kearney, Jennifer A.

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Modifier genes for sudden cardiac death von Schwartz, Peter J, Crotti, Lia, George, Alfred L

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Molecular and genetic basis of sudden cardiac death von George, Jr, Alfred L

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Predicting the functional impact of KCNQ1 variants with artificial neural networks von Phul, Saksham, Kuenze, Georg, Vanoye, Carlos G, Sanders, Charles R, George, Jr, Alfred L, Meiler, Jens

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ZFAND5/ZNF216 is an activator of the 26S proteasome that stimulates overall protein degradation von Lee, Donghoon, Takayama, Shinichi, Goldberg, Alfred L.

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Physiological genomics identifies genetic modifiers of long QT syndrome type 2 severity von Chai, Sam, Wan, Xiaoping, Ramirez-Navarro, Angelina, Tesar, Paul J, Kaufman, Elizabeth S, Ficker, Eckhard, George, Jr, Alfred L, Deschênes, Isabelle

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Novel mouse model of alternating hemiplegia of childhood exhibits prominent motor and seizure phenotypes von Hawkins, Nicole A., DeKeyser, Jean-Marc, Kearney, Jennifer A., George, Alfred L.

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26S proteasomes become stably activated upon heat shock when ubiquitination and protein degradation increase von Lee, Donghoon, Goldberg, Alfred L

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The influence of skeletal muscle on systemic aging and lifespan von Demontis, Fabio, Piccirillo, Rosanna, Goldberg, Alfred L., Perrimon, Norbert

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Multiple myeloma cells are exceptionally sensitive to heat shock, which overwhelms their proteostasis network and induces apoptosis von Sha, Zhe, Goldberg, Alfred L.

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Elucidating arrhythmogenic mechanisms of long-QT syndrome CALM1-F142L mutation in patient-specific induced pluripotent stem cell-derived cardiomyocytes von Rocchetti, Marcella, Sala, Luca, Dreizehnter, Lisa, Crotti, Lia, Sinnecker, Daniel, Mura, Manuela, Pane, Luna Simona, Altomare, Claudia, Torre, Eleonora, Mostacciuolo, Gaspare, Severi, Stefano, Porta, Alberto, De Ferrari, Gaetano M, George, Jr, Alfred L, Schwartz, Peter J, Gnecchi, Massimiliano, Moretti, Alessandra, Zaza, Antonio

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